GERSTMANN-STRAUSSLER-SCHEINKER DISEASE .2. NEUROFIBRILLARY TANGLES AND PLAQUES WITH PRP-AMYLOID COEXIST IN AN AFFECTED FAMILY

被引:166
作者
GHETTI, B
TAGLIAVINI, F
MASTERS, CL
BEYREUTHER, K
GIACCONE, G
VERGA, L
FARLOW, MR
CONNEALLY, PM
DLOUHY, SR
AZZARELLI, B
BUGIANI, O
机构
[1] INDIANA UNIV,SCH MED,DEPT NEUROL,INDIANAPOLIS,IN 46202
[2] INDIANA UNIV,SCH MED,DEPT MED GENET,INDIANAPOLIS,IN 46202
[3] IST C BESTA,DIV NEUROPATHOL,MILAN,ITALY
[4] UNIV MELBOURNE,DEPT PATHOL,PARKVILLE,VIC 3052,AUSTRALIA
[5] UNIV HEIDELBERG,ZENTRUM MOLEK BIOL HEIDELBERG,D-6900 HEIDELBERG,FED REP GER
关键词
D O I
10.1212/WNL.39.11.1453
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:1453 / 1461
页数:9
相关论文
共 59 条
[1]   FAMILIAL CEREBRAL AMYLOIDOSIS AND SPONGIFORM ENCEPHALOPATHY [J].
ADAM, J ;
CROW, TJ ;
DUCHEN, LW ;
SCARAVILLI, F ;
SPOKES, E .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1982, 45 (01) :37-45
[2]   CEREBELLAR PLAQUES IN FAMILIAL ALZHEIMERS-DISEASE (GERSTMANN-STRAUSSLER-SCHEINKER VARIANT-QUESTIONABLE) [J].
AZZARELLI, B ;
MULLER, J ;
GHETTI, B ;
DYKEN, M ;
CONNEALLY, PM .
ACTA NEUROPATHOLOGICA, 1985, 65 (3-4) :235-246
[3]   TOPOGRAPHIC DISTRIBUTION OF NEUROFIBRILLARY TANGLES AND GRANULOVACUOLAR DEGENERATION IN HIPPOCAMPAL CORTEX OF AGING AND DEMENTED PATIENTS - QUANTITATIVE STUDY [J].
BALL, MJ .
ACTA NEUROPATHOLOGICA, 1978, 42 (02) :73-80
[4]   ANTIBODIES TO A SCRAPIE PRION PROTEIN [J].
BENDHEIM, PE ;
BARRY, RA ;
DEARMOND, SJ ;
STITES, DP ;
PRUSINER, SB .
NATURE, 1984, 310 (5976) :418-421
[5]   SUB-ACUTE SPONGIFORM ENCEPHALOPATHY WITH MULTIFORM PLAQUE-FORMATION - PECULIAR FAMILIAL HEREDITARY-DISEASE OF CNS [SPINOCEREBELLAR ATROPHY WITH DEMENTIA, PLAQUES, AND PLAQUE-LIKE DEPOSITS IN CEREBELLUM AND CEREBRUM (GERSTMANN, STRAUSSLER, SCHEINKER)] [J].
BOELLAARD, JW ;
SCHLOTE, W .
ACTA NEUROPATHOLOGICA, 1980, 49 (03) :205-212
[6]   IDENTIFICATION OF A PROTEIN THAT PURIFIES WITH THE SCRAPIE PRION [J].
BOLTON, DC ;
MCKINLEY, MP ;
PRUSINER, SB .
SCIENCE, 1982, 218 (4579) :1309-1311
[7]   SCRAPIE PRP 27-30 IS A SIALOGLYCOPROTEIN [J].
BOLTON, DC ;
MEYER, RK ;
PRUSINER, SB .
JOURNAL OF VIROLOGY, 1985, 53 (02) :596-606
[8]  
Brion J. P., 1985, ARCH BIOL BRUX, V95, P229
[9]   UBIQUITIN PROTEIN CONJUGATES IN ALZHEIMERS LESIONS [J].
COLE, GM ;
TIMIRAS, PS .
NEUROSCIENCE LETTERS, 1987, 79 (1-2) :207-212
[10]   ATYPICAL GERSTMANN-STRAUSSLER SYNDROME OR FAMILIAL SPINOCEREBELLAR ATAXIA AND ALZHEIMERS-DISEASE [J].
DECOURTENMYERS, G ;
MANDYBUR, TI .
NEUROLOGY, 1987, 37 (02) :269-275