REDUCED REGIONAL CEREBRAL METABOLIC-RATE FOR GLUCOSE AT THE TERMINAL STAGE IN A CASE OF LATE INFANTILE NEURONAL CEROID LIPOFUSCINOSIS

被引:7
作者
FUEKI, N
IINUMA, K
KOJIMA, A
YANAI, K
HAGINOYA, K
TADA, K
IDO, T
ITO, M
机构
[1] TOHOKU UNIV,SCH MED,DEPT PEDIAT,SENDAI,MIYAGI 980,JAPAN
[2] TOHOKU UNIV,CTR CYCLOTRON & RADIOISOTOPE,DIV RADIOPHARMACEUT CHEM,SENDAI,MIYAGI 980,JAPAN
[3] TOHOKU UNIV,CTR CYCLOTRON & RADIOISOTOPE,DIV NUCL,SENDAI,MIYAGI 980,JAPAN
关键词
D O I
10.1177/088307389000500205
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Regional cerebral metabolic rate for glucose was determined for six different areas of the gray matter in an 8-year-old girl with late infantile neuronal ceroid lipofuscinosis. In all regions, the rates were almost half of the control values. The regional cerebral metabolic rate for glucose was relatively preserved in the striatal region and severely reduced in the frontal cortex. (J Child Neurol 1990;5:98-100). © 1990, Sage Publications. All rights reserved.
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页码:98 / 100
页数:3
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