STORAGE OF LIPOFUSCIN IN NEURONS IN MUCOPOLYSACCHARIDOSIS - REPORT ON A CASE OF SANFILIPPOS SYNDROME WITH HISTOCHEMICAL AND ELECTRON-MICROSCOPIC FINDINGS

被引:31
作者
OLDFORS, A
SOURANDER, P
机构
关键词
D O I
10.1007/BF00697002
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:287 / 292
页数:6
相关论文
共 28 条
[1]  
Adams C.W.M., 1965, NEUROCHEMISTRY
[2]  
BJORKERUD S, 1963, J ULTRASTR RES S, V5
[3]  
BORJESON M, 1969, Nordisk Medicin, V81, P567
[4]  
BRUNK UT, 1981, AGE PIGMENTS, pCH8
[5]   MUCOPOLYSACCHARIDOSIS-III-A (SANFILIPPO DISEASE TYPE-A) - HISTOCHEMICAL, ELECTRON MICROSCOPICAL AND BIOCHEMICAL FINDINGS [J].
CAIN, H ;
EGNER, E ;
KRESSE, H .
BEITRAGE ZUR PATHOLOGIE, 1977, 160 (01) :58-72
[6]   NEUROCHEMISTRY OF MUCOPOLYSACCHARIDOSES - BRAIN GLYCOSAMINOGLYCANS IN NORMALS AND 4 TYPES OF MUCOPOLYSACCHARIDOSES [J].
CONSTANTOPOULOS, G ;
MCCOMB, RD ;
DEKABAN, AS .
JOURNAL OF NEUROCHEMISTRY, 1976, 26 (05) :901-&
[7]   NEUROCHEMISTRY OF MUCOPOLYSACCHARIDOSES - BRAIN LIPIDS AND LYSOSOMAL ENZYMES IN PATIENTS WITH 4 TYPES OF MUCOPOLYSACCHARIDOSIS AND IN NORMAL CONTROLS [J].
CONSTANTOPOULOS, G ;
DEKABAN, AS .
JOURNAL OF NEUROCHEMISTRY, 1978, 30 (05) :965-973
[8]   MUCOPOLYSACCHARIDOSIS TYPE-IH, TYPE-IS, TYPE-II, AND TYPE-IIIA - GLYCOSAMINOGLYCANS AND LIPIDS OF ISOLATED BRAIN-CELLS AND OTHER FRACTIONS FROM AUTOPSIED TISSUES [J].
CONSTANTOPOULOS, G ;
IQBAL, K ;
DEKABAN, AS .
JOURNAL OF NEUROCHEMISTRY, 1980, 34 (06) :1399-1411
[9]   MUCOPOLYSACCHARIDOSIS TYPES-1, TYPE-2, TYPE-3A AND TYPE-5 - PATHOLOGICAL AND BIOCHEMICAL ABNORMALITIES IN NEURAL AND MESENCHYMAL ELEMENTS OF BRAIN [J].
DEKABAN, AS ;
CONSTANTOPOULOS, G .
ACTA NEUROPATHOLOGICA, 1977, 39 (01) :1-7
[10]  
DEKABAN AS, 1971, ARCH PATHOL, V91, P434