ABNORMAL BREAKDOWN OF ALPHA2-MACROGLOBULIN-TRYPSIN COMPLEX IN CYSTIC-FIBROSIS

被引：28

作者：

SHAPIRA, E ^{[1
]}

BENYOSEPH, Y ^{[1
]}

NADLER, HL ^{[1
]}

机构：

[1] NORTHWESTERN UNIV,CHILDRENS MEM HOSP,MED SCH,DEPT PEDIAT,DIV GENET,CHICAGO,IL 60614

来源：

CLINICA CHIMICA ACTA | 1977年 / 78卷 / 03期

关键词：

D O I：

10.1016/0009-8981(77)90068-7

中图分类号：

R446 [实验室诊断]; R-33 [实验医学、医学实验];

学科分类号：

1001 ;

摘要：

引用

页码：359 / 363

页数：5

共 10 条

[1]

BARETT AJ, 1973, BIOCHEM J, V133, P709

[2] STUDIES ON ELASTASE-SERUM PROTEIN INTERACTION .2. ON DIGESTION OF HUMAN ALPHA2-MACROGLOBULIN, AN ELASTASE INHIBITOR, BY ELASTASE [J].

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[6]

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[7]

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[8] ABSENCE OF AN ALPHA-2-MACROGLOBULIN-PROTEASE COMPLEX IN CYSTIC-FIBROSIS [J].

SHAPIRA, E ;

RAO, GJS ;

WESSEL, HU ;

NADLER, HL .

PEDIATRIC RESEARCH, 1976, 10 (09) :812-817

[9] DECREASED FORMATION OF ALPHA-2-MACROGLOBULIN-PROTEASE COMPLEXES IN PLASMA OF PATIENTS WITH CYSTIC-FIBROSIS [J].

SHAPIRA, E ;

BENYOSEPH, Y ;

NADLER, HL .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1976, 71 (03) :864-870

[10] STUDIES ON CYSTIC-FIBROSIS USING ISOELECTRIC FOCUSING .2. DEMONSTRATION OF DEFICIENT PROTEOLYTIC CLEAVAGE OF ALPHA2-MACROGLOBULIN IN CYSTIC-FIBROSIS PLASMA [J].

WILSON, GB ;

FUDENBERG, HH .

PEDIATRIC RESEARCH, 1976, 10 (02) :87-96

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