CHARACTERIZATION OF RESIDUAL ADENOSINE DEAMINATING ACTIVITY IN SPLEEN OF A PATIENT WITH COMBINED IMMUNODEFICIENCY DISEASE AND ADENOSINE-DEAMINASE DEFICIENCY

被引:71
作者
SCHRADER, WP [1 ]
POLLARA, B [1 ]
MEUWISSEN, HJ [1 ]
机构
[1] ALBANY MED COLL, DEPT PEDIAT, ALBANY, NY 12201 USA
关键词
D O I
10.1073/pnas.75.1.446
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:446 / 450
页数:5
相关论文
共 23 条
[1]  
AKEDO H, 1972, BIOCHIM BIOPHYS ACTA, V276, P257, DOI 10.1016/0005-2744(72)90028-9
[2]   ESTIMATION OF MOLECULAR WEIGHTS OF PROTEINS BY SEPHADEX GEL-FILTRATION [J].
ANDREWS, P .
BIOCHEMICAL JOURNAL, 1964, 91 (02) :222-+
[3]  
Brown JH, 1931, B JOHNS HOPKINS HOSP, V48, P69
[4]   PURIFICATION AND PROPERTIES OF CYTIDINE DEAMINASE FROM NORMAL AND LEUKEMIC GRANULOCYTES [J].
CHABNER, BA ;
JOHNS, DG ;
COLEMAN, CN ;
DRAKE, JC ;
EVANS, WH .
JOURNAL OF CLINICAL INVESTIGATION, 1974, 53 (03) :922-931
[5]  
CHEN SH, 1975, AM J HUM GENET, V27, P46
[6]  
DADDONA PE, 1977, J BIOL CHEM, V252, P110
[7]   ADENOSINE DEAMINASE ISOZYMES IN HUMAN TISSUES [J].
EDWARDS, YH ;
HOPKINSON, DA ;
HARRIS, H .
ANNALS OF HUMAN GENETICS, 1971, 35 (OCT) :207-+
[8]  
GIBLETT ER, 1972, LANCET, V2, P1067
[9]   CHARACTERIZATION OF RESIDUAL ENZYME-ACTIVITY IN FIBROBLASTS FROM PATIENTS WITH ADENOSINE DEAMINASE DEFICIENCY AND COMBINED IMMUNODEFICIENCY - EVIDENCE FOR A MUTANT ENZYME [J].
HIRSCHHORN, R ;
BERATIS, N ;
ROSEN, FS .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1976, 73 (01) :213-217
[10]   CONVERSION OF HUMAN ERYTHROCYTE-ADENOSINE DEAMINASE ACTIVITY TO DIFFERENT TISSUE-SPECIFIC ISOENZYMES - EVIDENCE FOR A COMMON CATALYTIC UNIT [J].
HIRSCHHORN, R .
JOURNAL OF CLINICAL INVESTIGATION, 1975, 55 (03) :661-667