SCHNITZLERS SYNDROME-ASSOCIATED WITH SENSORIMOTOR NEUROPATHY

被引:36
作者
LEBBE, C
RYBOJAD, M
KLEIN, F
OKSENHENDLER, E
CATALA, M
DANON, F
MOREL, P
机构
[1] HOP ST LOUIS,SERV IMMUNOHEMATOL,PARIS,FRANCE
[2] HOP LA PITIE SALPETRIERE,SERV NEUROL,PARIS,FRANCE
关键词
D O I
10.1016/S0190-9622(94)70031-1
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
We describe a patient with chronic urticaria in association with monoclonal IgM gammopathy (Schnitzler's syndrome). Seven years after the onset of the cutaneous lesions sensorimotor neuropathy developed. Myelin-associated glycoprotein was detected in the patient's serum. High doses of corticosteroids improved the skin condition but failed to prevent the neuropathy. Six months of treatment with immunoglobulins was without benefit.
引用
收藏
页码:316 / 318
页数:3
相关论文
共 28 条
  • [1] ALTMEYER P, 1977, Aktuelle Dermatologie, V3, P71
  • [2] BARRIERE H, 1976, SEM HOP PARIS, V52, P221
  • [3] BARRIERE H, 1974, B SOC FR DERMATOL SY, V81, P361
  • [4] SCHNITZLER SYNDROME - A BROADER CLINICAL SPECTRUM
    BERDY, SS
    BLOCH, KJ
    [J]. JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY, 1991, 87 (04) : 849 - 854
  • [5] URTICARIA WITH MACROGLOBULINEMIA - DISEASE-ACTIVITY ASSOCIATED ALTERATIONS IN IMMUNOGLOBULINS PROFILE AND BONE-MARROW HYPODIPLOIDY
    BONNETBLANC, JM
    DROUET, M
    LAPLAUD, P
    BEDANE, C
    BERNARD, P
    [J]. DERMATOLOGICA, 1990, 181 (01): : 41 - 43
  • [6] URTICARIAL VASCULITIS ASSOCIATED WITH A MONOCLONAL IGM GAMMOPATHY - SCHNITZLERS SYNDROME
    BORRADORI, L
    RYBOJAD, M
    PUISSANT, A
    DALLOT, A
    VEROLA, O
    MOREL, P
    [J]. BRITISH JOURNAL OF DERMATOLOGY, 1990, 123 (01) : 113 - 118
  • [7] BROUET JC, 1990, NOUV REV FR HEMATOL, V32, P307
  • [8] CHRONIC URTICARIA WITH MONOCLONAL IGM - A REPORT OF 5 CASES
    CLAUVEL, JP
    BROUET, JC
    DANON, F
    LEIBOWITCH, M
    SELIGMANN, M
    [J]. CLINICAL IMMUNOLOGY AND IMMUNOPATHOLOGY, 1982, 25 (03): : 348 - 353
  • [9] HIGH-DOSE INTRAVENOUS IMMUNOGLOBULIN IN THE TREATMENT OF DEMYELINATING NEUROPATHY ASSOCIATED WITH MONOCLONAL GAMMOPATHY
    COOK, D
    DALAKAS, M
    GALDI, A
    BIONDI, D
    PORTER, H
    [J]. NEUROLOGY, 1990, 40 (02) : 212 - 214
  • [10] DELLAGI K, 1983, BLOOD, V62, P280