MITOCHONDRIAL ENCEPHALOMYOPATHY (MELAS) - PATHOLOGICAL-STUDY AND SUCCESSFUL THERAPY WITH COENZYME-Q10 AND IDEBENONE

被引:152
作者
IHARA, Y
NAMBA, R
KURODA, S
SATO, T
SHIRABE, T
机构
[1] KAWASAKI MED SCH, DEPT NEUROPATHOL, KURASHIKI, OKAYAMA 70101, JAPAN
[2] OKAYAMA UNIV, SCH MED, DEPT NEUROPSYCHIAT, OKAYAMA 700, JAPAN
[3] JUNTENDO UNIV, SCH MED, DEPT NEUROL, TOKYO 113, JAPAN
关键词
D O I
10.1016/0022-510X(89)90112-3
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:263 / 271
页数:9
相关论文
共 12 条
  • [1] MITOCHONDRIAL MYOPATHY AND CARDIOMYOPATHY WITH NEURODEGENERATIVE FEATURES AND MULTIPLE BRAIN INFARCTS
    BOGOUSSLAVSKY, J
    PERENTES, E
    DERUAZ, JP
    REGLI, F
    [J]. JOURNAL OF THE NEUROLOGICAL SCIENCES, 1982, 55 (03) : 351 - 357
  • [2] MYOCLONUS EPILEPSY ASSOCIATED WITH RAGGED-RED FIBERS (MITOCHONDRIAL ABNORMALITIES) - DISEASE ENTITY OR A SYNDROME - LIGHT-MICROSCOPIC AND ELECTRON-MICROSCOPIC STUDIES OF 2 CASES AND REVIEW OF LITERATURE
    FUKUHARA, N
    TOKIGUCHI, S
    SHIRAKAWA, K
    TSUBAKI, T
    [J]. JOURNAL OF THE NEUROLOGICAL SCIENCES, 1980, 47 (01) : 117 - 133
  • [3] RETINITIS PIGMENTOSA, EXTERNAL OPHTHALMOPLEGIA, AND COMPLETE HEART BLOCK - UNUSUAL SYNDROME WITH HISTOLOGIC STUDY IN ONE OF 2 CASES
    KEARNS, TP
    SAYRE, GP
    [J]. ARCHIVES OF OPHTHALMOLOGY, 1958, 60 (02) : 280 - 289
  • [4] ULTRASTRUCTURAL-STUDY OF THE CHILDHOOD MITOCHONDRIAL MYOPATHIC SYNDROME ASSOCIATED WITH LACTIC-ACIDOSIS
    KOBAYASHI, Y
    MIYABAYASHI, S
    TAKADA, G
    NARISAWA, K
    TADA, K
    YAMAMOTO, TY
    [J]. EUROPEAN JOURNAL OF PEDIATRICS, 1982, 139 (01) : 25 - 30
  • [5] MITOCHONDRIAL ENCEPHALOMYOPATHY WITH LACTATE PYRUVATE ELEVATION AND BRAIN INFARCTIONS
    KURIYAMA, M
    UMEZAKI, H
    FUKUDA, Y
    OSAME, M
    KOIKE, K
    TATEISHI, J
    IGATA, A
    [J]. NEUROLOGY, 1984, 34 (01) : 72 - 77
  • [6] IMPROVEMENT OF ABNORMAL PYRUVATE METABOLISM AND CARDIAC CONDUCTION DEFECT WITH COENZYME-Q10 IN KEARNS-SAYRE SYNDROME
    OGASAHARA, S
    YORIFUJI, S
    NISHIKAWA, Y
    TAKAHASHI, M
    WADA, K
    HAZAMA, T
    NAKAMURA, Y
    HASHIMOTO, S
    KONO, N
    TARUI, S
    [J]. NEUROLOGY, 1985, 35 (03) : 372 - 377
  • [7] MITOCHONDRIAL ANGIOPATHY IN CEREBRAL BLOOD-VESSELS OF MITOCHONDRIAL ENCEPHALOMYOPATHY
    OHAMA, E
    OHARA, S
    IKUTA, F
    TANAKA, K
    NISHIZAWA, M
    MIYATAKE, T
    [J]. ACTA NEUROPATHOLOGICA, 1987, 74 (03) : 226 - 233
  • [8] MITOCHONDRIAL MYOPATHY, ENCEPHALOPATHY, LACTIC-ACIDOSIS, AND STROKELIKE EPISODES - A DISTINCTIVE CLINICAL SYNDROME
    PAVLAKIS, SG
    PHILLIPS, PC
    DIMAURO, S
    DEVIVO, DC
    ROWLAND, LP
    [J]. ANNALS OF NEUROLOGY, 1984, 16 (04) : 481 - 488
  • [9] INDEPENDENCE OF BLOOD AND CEREBROSPINAL FLUID LACTATE
    POSNER, JB
    PLUM, F
    [J]. ARCHIVES OF NEUROLOGY, 1967, 16 (05) : 492 - &
  • [10] SCHNEIDER H, 1982, J BIOL CHEM, V257, P789