INFERIOR VENA-CAVA THROMBOSIS IN A CHILD WITH NEPHROBLASTOMA AND COMBINED DEFICIENCY OF ANTITHROMBIN-III AND FREE PROTEIN-S

被引：7

作者：

DEMARMELS, F ^{[1
]}

LUTHY, AR ^{[1
]}

HIRT, A ^{[1
]}

FURLAN, M ^{[1
]}

LAMMLE, B ^{[1
]}

机构：

[1] UNIV BERN,INSELSPITAL,DEPT PEDIAT,CH-3010 BERN,SWITZERLAND

来源：

BLUT | 1990年 / 61卷 / 05期

关键词：

CAVAL VEIN THROMBOSIS; NEPHROBLASTOMA; ANTITHROMBIN-III DEFICIENCY; PROTEIN-S DEFICIENCY;

D O I：

10.1007/BF01732880

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

A 3 1/2-year-old girl developed thrombosis of the inferior caval and renal veins several weeks after complete resection of a nephroblastoma. Her mother had suffered from pulmonary embolism at the age of 18 years. Familial antithrombin III deficiency and persistently lowered free protein S levels in the proposita were found. It is assumed that the combination of these two regulatory defects of hemostasis contributed to the early occurrence of this severe thrombotic event.

引用

页码：295 / 297

页数：3

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