LIPOAMIDE DEHYDROGENASE IN FRIEDREICHS ATAXIA FIBROBLASTS

被引：18

作者：

MELANCON, SB

POTIER, M

DALLAIRE, L

FONTAINE, G

GRENIER, B

LEMIEUX, B

GEOFFROY, G

BARBEAU, A

机构：

[1] CLIN RES INST MONTREAL, 110 PINE AVE W, MONTREAL H2W 1R7, QUEBEC, CANADA

[2] HOP ST JUSTINE, PEDIAT RES CTR, MONTREAL 250, QUEBEC, CANADA

来源：

CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES | 1978年 / 5卷 / 01期

关键词：

D O I：

10.1017/S0317167100024884

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

引用

页码：115 / 118

页数：4

共 12 条

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MENON, NK .

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[2]

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[3] INHERITED DEFECT AFFECTING TRICARBOXYLIC ACID CYCLE IN A PATIENT WITH CONGENITAL LACTIC ACIDOSIS [J].

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HOM, E .

JOURNAL OF CLINICAL INVESTIGATION, 1972, 51 (07) :1845-&

[4]

LEMIEUX B, 1976, Canadian Journal of Neurological Sciences, V3, P373

[5] ALPHA-KETO ACID DEHYDROGENASE COMPLEXES .11. COMPARATIVE STUDIES OF REGULATORY PROPERTIES OF PYRUVATE DEHYDROGENASE COMPLEXES FROM KIDNEY, HEART, AND LIVER MITOCHONDRIA [J].

LINN, TC ;

PETTIT, FH ;

HUCHO, F ;

REED, LJ .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1969, 64 (01) :227-&

[6]

MELANCON SB, 1977, PEDIATR RES, V11, P460, DOI 10.1203/00006450-197704000-00541

[7]

MELANCON SB, 1972, P SOC EXP BIOL MED, V141, P391

[8]

MELANCON SB, 1973, METHODS NEUROCHEMIST, P1

[9]

PELLEY JW, 1976, CLIN CHEM, V22, P275

[10] MACROMOLECULAR ORGANIZATION OF ENZYME SYSTEMS [J].

REED, LJ .

ANNUAL REVIEW OF BIOCHEMISTRY, 1966, 35 :57-&

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