OCCURRENCE OF BETA-GLUCOCEREBROSIDASE ACTIVITY IN GLUCOCEREBROSIDE-RICH DEPOSITS OF GAUCHERS-DISEASE

被引：9

作者：

GLEW, RH

CHRISTOPHER, AR

SCHNURE, FW

LEE, RE

机构：

[1] UNIV PITTSBURGH, SCH MED, DEPT BIOCHEM, PITTSBURGH, PA 15261 USA

[2] UNIV PITTSBURGH, SCH MED, DEPT PATHOL, PITTSBURGH, PA 15261 USA

来源：

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS | 1974年 / 160卷 / 01期

关键词：

D O I：

10.1016/S0003-9861(74)80022-6

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：162 / 167

页数：6

共 13 条

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SHAPIRO, D .

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[3] DEMONSTRATION OF A DEFICIENCY OF GLUCOCEREBROSIDE-CLEAVING ENZYME IN GAUCHERS DISEASE [J].

BRADY, RO ;

KANFER, JN ;

BRADLEY, RM ;

SHAPIRO, D .

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[4] SPHINGOLIPIDOSES [J].

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[6]

GLEW RH, IN PRESS

[7]

HUGGETT ASG, 1957, LANCET, V2, P368

[8]

KUSKE TT, 1971, J LIPID RES, V12, P173

[9] FINE STRUCTURE OF CEREBROSIDE OCCURRING IN GAUCHERS DISEASE [J].

LEE, RE .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1968, 61 (02) :484-&

[10]

LOWRY OH, 1951, J BIOL CHEM, V193, P265

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