BASAL GANGLIA CALCIFICATION IN KEARNS-SAYRE SYNDROME

被引：31

作者：

ROBERTSON, WC

VISESKUL, C

LEE, YE

LLOYD, RV

机构：

[1] UNIV WISCONSIN,DEPT NEUROL,MADISON,WI 53706

[2] UNIV WISCONSIN,DEPT PATHOL,MADISON,WI 53706

来源：

ARCHIVES OF NEUROLOGY | 1979年 / 36卷 / 11期

关键词：

D O I：

10.1001/archneur.1979.00500470081017

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

The Kearns-Sayre syndrome (KSS) appears to be a distinctive disorder characterized by progressive external ophthalmoplegia, pigmentary degeneration of the retina, heart block, and elevated CSF protein levels. Recent reports have suggested that abnormalities of muscle mitochondria may also be a consistent finding in KSS. We recently examined a patient with KSS whose skeletal muscle contained abnormal mitochondria. In addition, a computerized tomographic scan of the head showed cerebellar and brain stem atrophy, as well as calcification in the region of the basal ganglia. © 1979, American Medical Association. All rights reserved.

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页码：711 / 713

页数：3

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