PERSISTENT MULLERIAN DUCT SYNDROME WITH TRANSVERSE TESTICULAR ECTOPIA AND SPERMATOGENESIS

被引：46

作者：

MARTIN, EL

BENNETT, AH

CROMIE, WJ

机构：

[1] Division of Urological Surgery, Albany Medical Center Hospital, Albany, NY

来源：

JOURNAL OF UROLOGY | 1992年 / 147卷 / 06期

关键词：

GONADAL DYSGENESIS; PSEUDOHERMAPHRODITISM; MULLERIAN DUCTS; TESTIS;

D O I：

10.1016/S0022-5347(17)37646-2

中图分类号：

R5 [内科学]; R69 [泌尿科学（泌尿生殖系疾病）];

学科分类号：

1002 ; 100201 ;

摘要：

Normal male sexual differentiation is dependent on at least 2 factors: 1) testosterone and 2) mullerian inhibiting factor. The absence of mullerian inhibiting factor is responsible for a rare form of male pseudohermaphroditism, the persistent mullerian duct syndrome or hernia uteri inguinale. Patients with this syndrome present with persistent mullerian structures and the syndrome may be associated with transverse testicular ectopia. Additionally, most patients have azoospermia. We report a case of persistent mullerian duct syndrome with transverse testicular ectopia in which sperm are documented in the ejaculate.

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页码：1615 / 1617

页数：3

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