HEREDITARY GINGIVAL FIBROMATOSIS - REPORT OF AN EXTENSIVE 4-GENERATION PEDIGREE

被引:51
作者
BOZZO, L
DEALMEIDA, OP
SCULLY, C
ALDRED, MJ
机构
[1] UNIV QUEENSLAND, DEPT DENT, BRISBANE, QLD 4072, AUSTRALIA
[2] UNIV CAMPINAS, FAC ODONTOL PIRACICABA, DEPT ORAL PATHOL, PIRACICABA, BRAZIL
[3] UCL EASTMAN DENT INST ORAL & DENT HEALTHCARE SCI, LONDON, ENGLAND
来源
ORAL SURGERY ORAL MEDICINE ORAL PATHOLOGY ORAL RADIOLOGY AND ENDODONTOLOGY | 1994年 / 78卷 / 04期
关键词
D O I
10.1016/0030-4220(94)90037-X
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
A Brazilian family with hereditary gingival fibromatosis is described with multiple affected subjects in four generations. A total of 50 (48%), of 105 at-risk offspring in a family of 132 members were affected, consistent with an autosomal dominant mode of inheritance. This family appears to represent the largest pedigree with this condition reported in the literature.
引用
收藏
页码:452 / 454
页数:3
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