EFFECT OF THIAMINE TREATMENT ON ACTIVITY OF PYRUVATE DEHYDROGENASE - RELATION TO TREATMENT OF LEIGHS ENCEPHALOMYELOPATHY

被引：18

作者：

HOMMES, FA ^{[1
]}

BERGER, R ^{[1
]}

LUITDEHA.G ^{[1
]}

机构：

[1] UNIV GRONINGEN, SCH MED, DEPT PEDIATR, LAB DEV BIOCHEM, GRONINGEN, NETHERLANDS

来源：

关键词：

D O I：

10.1203/00006450-197307000-00003

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：616 / 619

页数：4

共 18 条

[1] BERGER R, 1972, 8 M EUR BIOCH SOC AM
[2] SIMPLE AND RAPID ASSAY OF OXIDATIVE PHOSPHORYLATION
CHANCE, B
WILLIAMS, GR
[J]. NATURE, 1955, 175 (4469) : 1120 - 1121
[3] THIAMINE TRIPHOSPHATE DEFICIENCY IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY
COOPER, JR
ITOKAWA, Y
PINCUS, JH
[J]. SCIENCE, 1969, 164 (3875) : 74 - &
[4] EXPERIENCE WITH PHOSPHORYL TRANSFERASE INHIBITION IN SUBACUTE NECROTIZING ENCEPHALOMYELOPATHY
COOPER, JR
PINCUS, JH
ITOKAWA, Y
PIROS, K
[J]. NEW ENGLAND JOURNAL OF MEDICINE, 1970, 283 (15) : 793 - &
[5] DEGROOT CJ, 1972, FURTHER STUDIES LEIG, P40
[6] DELVIN E, 1972, PEDIATR RES, V6, P392
[7] DIFFERENCES BETWEEN ATP/ADP RATIOS IN MITOCHONDRIAL MATRIX AND IN EXTRAMITOCHONDRIAL SPACE
HELDT, HW
MILOVANCEV, M
KLINGENBERG, M
[J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1972, 30 (03): : 434 - +
[8] LEIGHS ENCEPHALOMYELOPATHY - AN INBORN ERROR OF GLUCONEOGENESIS
HOMMES, FA
POLMAN, HA
REERINK, JD
[J]. ARCHIVES OF DISEASE IN CHILDHOOD, 1968, 43 (230) : 423 - &
[9] HOMMES FA, BIOCHEMISTRY INBORN
[10] LANSDALE D, 1968, NEW ENGL J MED, V278, P1235