ANTENATAL DETECTION OF CONGENITAL DIAPHRAGMATIC-HERNIAS - THE NORTHERN REGION EXPERIENCE

被引:32
作者
DILLON, E [1 ]
RENWICK, M [1 ]
机构
[1] NO REG HLTH AUTHOR,NO REG FETAL ABNORMAL SURVEY STEERING GRP,NEWCASTLE TYNE,ENGLAND
关键词
D O I
10.1016/S0009-9260(05)81015-3
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
This study analyses 7 years of data relating to congenital diaphragmatic herniation in the Northern Region. Ninety-nine confirmed cases were notified to the Northern Region Fetal Abnormality Survey between 1985 and 1991, which is an incidence of 0.35 per 1000 births. A specific diagnosis of CDH was made by antenatal ultrasound in 21 fetuses. The rate of detection improved from 6% to 41% but this had no impact on survival; severe pulmonary hypoplasia was found in the majority dying in the first 48 h. Another structural abnormality occurred in 29% and was the primary antenatal scan diagnosis in 11 fetuses. No other reliable indicator of outcome was identified, including the gestation when detected. The incidence of chromosomal abnormality was 5% and Fryns' syndrome 4%.
引用
收藏
页码:264 / 267
页数:4
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