REYES-SYNDROME IN AN ADULT

被引:10
作者
VANHOLDER, R
DEREUCK, J
SIEBENPRAET, M
DECOSTER, W
机构
[1] STATE UNIV GHENT,DEPT INTENS CARE,B-9000 GHENT,BELGIUM
[2] STATE UNIV GHENT,DEPT NEUROL,NEUROPATHOL UNIT,B-9000 GHENT,BELGIUM
[3] STATE UNIV GHENT,DEPT PATHOL,B-9000 GHENT,BELGIUM
关键词
D O I
10.1159/000115106
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Reye's syndrome or encephalopathy with fatty infiltration of the liver occurs mainly in childhood and to a lesser degree in adult age. This report concerns a rare adult case of this syndrome in Europe. The different diagnostic steps are described, with special emphasis on the enzymatic disturbances of the Krebs-Henseleit cycle and on the morphological criteria needed to confirm the diagnosis.
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收藏
页码:367 / 372
页数:6
相关论文
共 20 条
[1]   REYES SYNDROME - PATIENT SERUM ALTERS MITOCHONDRIAL-FUNCTION AND MORPHOLOGY INVITRO [J].
APRILLE, JR .
SCIENCE, 1977, 197 (4306) :908-910
[2]  
BOVE KE, 1975, GASTROENTEROLOGY, V69, P685
[3]   HEPATIC DEGENERATION AND DYSFUNCTION IN REYES SYNDROME [J].
BROWN, RE ;
MADGE, GE .
AMERICAN JOURNAL OF DIGESTIVE DISEASES, 1971, 16 (12) :1116-&
[4]   TRANSIENTLY REDUCED ACTIVITY OF CARBAMYL-PHOSPHATE SYNTHETASE AND ORNITHINE TRANSCARBAMYLASE IN LIVER OF CHILDREN WITH REYES SYNDROME [J].
BROWN, T ;
HUG, G ;
LANSKY, L ;
BOVE, K ;
SCHEVE, A ;
RYAN, M ;
BROWN, H ;
SCHUBERT, WK ;
PARTIN, JC ;
LLOYDSTILL, J .
NEW ENGLAND JOURNAL OF MEDICINE, 1976, 294 (16) :861-867
[5]   HETEROGENOUS MUTATIONS OF STRUCTURAL GENE OF HUMAN ORNITHINE CARBAMYLTRANSFERASE AS OBSERVED IN 5 PERSONAL CASES [J].
CATHELINEAU, L ;
SAUDUBRAY, JM ;
POLONOVSKI, C .
ENZYME, 1974, 18 (1-2) :103-113
[6]   NATIONWIDE OUTBREAK OF REYES SYNDROME - ITS EPIDEMIOLOGIC RELATIONSHIP TO INFLUENZA B [J].
COREY, L ;
RUBIN, RJ ;
HATTWICK, MAW ;
NOBLE, GR ;
CASSIDY, E .
AMERICAN JOURNAL OF MEDICINE, 1976, 61 (05) :615-625
[7]   REYES SYNDROME .2. OCCURRENCE IN ABSENCE OF SEVERE FATTY INFILTRATION OF LIVER [J].
GLASGOW, AM ;
COTTON, RB ;
BOURGEOIS, CH ;
DHIENSIRI, K .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1972, 124 (06) :834-836
[8]   LEAN REYE SYNDROME [J].
GLICK, TH .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1973, 125 (06) :900-901
[9]  
GOSSEYE S, 1973, ARCH FR PEDIATR, V30, P381
[10]  
HUTTENLO.PR, 1969, PEDIATRICS, V43, P443