RHABDOMYOSARCOMAS DEVELOPING IN ASSOCIATION WITH MEDIASTINAL GERM-CELL TUMORS

被引:19
作者
CABALLERO, C [1 ]
GOMEZ, S [1 ]
MATIASGUIU, X [1 ]
PRAT, J [1 ]
机构
[1] AUTONOMOUS UNIV BARCELONA,HOSP SANTA CREU & SANT PAU,DEPT PATHOL,AVGDA SANT ANTONI M CLARET 167,E-08025 BARCELONA,SPAIN
关键词
GERM CELL TUMOR; RHABDOMYOSARCOMA; MEDIASTINUM;
D O I
10.1007/BF01600260
中图分类号
R602 [外科病理学、解剖学]; R32 [人体形态学];
学科分类号
100101 ;
摘要
Two mediastinal rhabdomyosarcomas that arose in association with germ cell tumours are reported. One presented as a small component of a mixed germ cell tumour with yolk sac and immature teratomatous elements. The other appeared as a large mass 4 months after diagnosis of a yolk sac carcinoma that had been treated with chemotherapy. The first patient was alive and free of disease 7 years later, whereas the second died of tumour 3 months post-operatively. The proportion of rhabdomyosarcoma within the germ cell tumours appears to have influenced the prognosis of these patients. This observation emphasizes the necessity of performing a thorough search for sarcomatous elements and quantifying their relative proportion in germ cell tumours of the mediastinum.
引用
收藏
页码:539 / 543
页数:5
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