CHRONIC SENSORY DEMYELINATING NEUROPATHY - CHRONIC INFLAMMATORY DEMYELINATING POLYNEUROPATHY PRESENTING AS A PURE SENSORY NEUROPATHY

被引:136
作者
OH, SJ [1 ]
JOY, JL [1 ]
KURUOGLU, R [1 ]
机构
[1] VET ADM MED CTR,BIRMINGHAM,AL 35233
关键词
D O I
10.1136/jnnp.55.8.677
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
The clinical electrophysiological and histological features of 10 cases of "chronic sensory demyelinating neuropathy" (CSDN) are reported. This entity is characterised by: 1) subacute or chronic progression; 2) pure sensory neuropathy; 3) high spinal fluid protein in the majority of cases; 4) electrophysiological evidence of demyelination affecting motor as well as sensory nerve fibres; 5) demyelination on sural nerve biopsy and 6) good response to immunotherapy in progressive phase. It is believed that this entity represents chronic inflammatory demyelinating polyneuropathy (CIDP) presenting as pure sensory neuropathy.
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页码:677 / 680
页数:4
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