INTRA-GASTRIC FEEDING IN TYPE-I GLYCOGEN-STORAGE DISEASE - FACTORS AFFECTING THE CONTROL OF LACTIC ACIDEMIA

被引:26
作者
STANLEY, CA [1 ]
MILLS, JL [1 ]
BAKER, L [1 ]
机构
[1] UNIV PENN,SCH MED,DEPT PEDIAT,DIV ENDOCRINOL DIABET,PHILADELPHIA,PA 19104
关键词
D O I
10.1203/00006450-198112000-00010
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:1504 / 1508
页数:5
相关论文
共 16 条
[1]   MEASUREMENT OF TRUE GLUCOSE PRODUCTION-RATES IN INFANCY AND CHILDHOOD WITH 6,6-DIDEUTEROGLUCOSE [J].
BIER, DM ;
LEAKE, RD ;
HAYMOND, MW ;
ARNOLD, KJ ;
GRUENKE, LD ;
SPERLING, MA ;
KIPNIS, DM .
DIABETES, 1977, 26 (11) :1016-1023
[2]   DECREASED KETOGENESIS IN VONGIERKES DISEASE (TYPE-I GLYCOGENOSIS) [J].
BINKIEWICZ, A ;
SENIOR, B .
JOURNAL OF PEDIATRICS, 1973, 83 (06) :973-978
[3]   COMPARISON OF EFFECTS OF TOTAL PARENTERAL NUTRITION, CONTINUOUS INTRAGASTRIC FEEDING, AND PORTACAVAL-SHUNT ON A PATIENT WITH TYPE-I GLYCOGEN-STORAGE DISEASE [J].
BURR, IM ;
ONEILL, JA ;
KARZON, DT ;
HOWARD, LJ ;
GREENE, HL .
JOURNAL OF PEDIATRICS, 1974, 85 (06) :792-795
[4]   NOCTURNAL INTRA-GASTRIC INFUSION OF GLUCOSE IN MANAGEMENT OF DEFECTIVE GLUCONEOGENESIS WITH HYPOGLYCEMIA [J].
EHRLICH, RM ;
ROBINSON, BH ;
FREEDMAN, MH ;
HOWARD, NJ .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1978, 132 (03) :241-243
[5]   KETOSIS IN HEPATIC GLYCOGENOSIS [J].
FERNANDES, J ;
PIKAAR, NA .
ARCHIVES OF DISEASE IN CHILDHOOD, 1972, 47 (251) :41-+
[6]  
FERNANDES J, 1979, PEDIATR RES, V13, P25
[7]  
Greene H L, 1979, Adv Pediatr, V26, P63
[8]   CONTINUOUS NOCTURNAL INTRAGASTRIC FEEDING FOR MANAGEMENT OF TYPE-1 GLYCOGEN-STORAGE DISEASE [J].
GREENE, HL ;
SLONIM, AE ;
ONEILL, JA ;
BURR, IM .
NEW ENGLAND JOURNAL OF MEDICINE, 1976, 294 (08) :423-425
[9]   TYPE-I GLYCOGEN-STORAGE DISEASE - 5 YEARS OF MANAGEMENT WITH NOCTURNAL INTRA-GASTRIC FEEDING [J].
GREENE, HL ;
SLONIM, AE ;
BURR, IM ;
MORAN, JR .
JOURNAL OF PEDIATRICS, 1980, 96 (03) :590-595
[10]  
HAVEL JR, 1969, T ASS AM PHYS, V82, P305