PROLIDASE DEFICIENCY WITH IMINODIPEPTIDURIA - BIOCHEMICAL INVESTIGATIONS AND 1ST RESULTS OF ATTEMPTED THERAPY

被引:26
作者
CHARPENTIER, C
DAGBOVIE, K
LEMONNIER, A
LARREGUE, M
JOHNSTONE, RAW
机构
[1] CTR HOSP UNIV POITIERS,F-86021 POITIERS,FRANCE
[2] ROBERT ROBINSON LABS,LIVERPOOL L69 3BX,ENGLAND
关键词
D O I
10.1007/BF02263599
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:77 / 78
页数:2
相关论文
共 8 条
[1]   PROLIDASE DEFICIENCY - DERMATOLOGICAL MANIFESTATIONS AND SOME ADDITIONAL BIOCHEMICAL STUDIES [J].
ARATA, J ;
UMEMURA, S ;
YAMAMOTO, Y ;
HAGIYAMA, M ;
NOHARA, N .
ARCHIVES OF DERMATOLOGY, 1979, 115 (01) :62-67
[2]   FURTHER STUDIES ON A PATIENT WITH IMINODIPEPTIDURIA - PROBABLE CASE OF PROLIDASE DEFICIENCY [J].
BUIST, NRM ;
BELLINGE.JF ;
KENNAWAY, NG ;
STRANDHO.JJ .
METABOLISM-CLINICAL AND EXPERIMENTAL, 1972, 21 (12) :1113-&
[3]   ULTRAMICROTECHNIQUE FOR DETECTION AND SEPARATION OF SMALL MOLECULAR-WEIGHT PEPTIDES FROM AMINO-ACIDS [J].
GALLOTORRES, HE ;
LUDORF, J ;
MILLER, ON .
ANALYTICAL BIOCHEMISTRY, 1975, 64 (01) :260-267
[4]   A SYNDROME RESEMBLING LATHYRISM ASSOCIATED WITH IMINODIPEPTIDURIA [J].
GOODMAN, SI ;
SOLOMONS, CC ;
MUSCHENHEIM, F ;
MCINTYRE, CA ;
MILES, B ;
OBRIEN, D .
AMERICAN JOURNAL OF MEDICINE, 1968, 45 (01) :152-+
[5]   PROLIDASE DEFICIENCY WITH IMIDODIPEPTIDURIA - FAMILIAL CASE WITH AND WITHOUT CLINICAL SYMPTOMS [J].
ISEMURA, M ;
HANYU, T ;
GEJYO, F ;
NAKAZAWA, R ;
IGARASHI, R ;
MATSUO, S ;
IKEDA, K ;
SATO, Y .
CLINICA CHIMICA ACTA, 1979, 93 (03) :401-407
[6]  
JACKSON SH, 1975, CAN MED ASSOC J, V113, P759
[7]   PROLIDASE DEFICIENCY IN MAN WITH IMINOPEPTIDURIA [J].
POWELL, GF ;
RASCO, MA ;
MANISCALCO, RM .
METABOLISM-CLINICAL AND EXPERIMENTAL, 1974, 23 (06) :505-513
[8]   IMINOPEPTIDURIA, SKIN ULCERATIONS, AND EDEMA IN A BOY WITH PROLIDASE DEFICIENCY [J].
SHEFFIELD, LJ ;
SCHLESINGER, P ;
FAULL, K ;
HALPERN, BJ ;
SCHIER, GM ;
COTTON, RGH ;
HAMMOND, J ;
DANKS, DM .
JOURNAL OF PEDIATRICS, 1977, 91 (04) :578-583