NEW UNSTABLE HAEMOGLOBIN BORAS - BETA88 (F4) LEUCINE-]ARGININE

被引:33
作者
HOLLENDER, A
LORKIN, PA
LEHMANN, H
SVENSSON, B
机构
[1] Department of Clinical Chemistry, Lidköping
[2] MRC Abnormal Haemoglobin Unit, University Department of Biochemistry
[3] Department of Geriatrics and Rehabilitation, Skara
关键词
D O I
10.1038/222953a0
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
Haemoglobin Bors has a mutation in which arginine is substituted for leucine in the haem pocket. The introduction of a positive charge into the haem pocket is probably avoided by the accommodation of the guanidinium group in an external crevice of the molecule. © 1969 Nature Publishing Group.
引用
收藏
页码:953 / +
页数:1
相关论文
共 12 条
[1]   HAEMOGLOBIN SYDNEY - BETA67(E11) VALINE -] ALANINE - AN ENERGING PATTERN OF UNSTABLE HAEMOGLOBINS [J].
CARRELL, RW ;
LEHMANN, H ;
LORKIN, PA ;
RAIK, E ;
HUNTER, E .
NATURE, 1967, 215 (5101) :626-&
[2]   ABNORMAL HUMAN HAEMOGLOBINS - SEPARATION AND CHARACTERIZATION OF ALPHA AND BETA CHAINS BY CHROMATOGRAPHY AND DETERMINATION OF 2 NEW VARIANTS HB CHESAPEAKE AND HB J (BANGKOK) [J].
CLEGG, JB ;
NAUGHTON, MA ;
WEATHERA.DJ .
JOURNAL OF MOLECULAR BIOLOGY, 1966, 19 (01) :91-&
[3]   HEREDITARY HEINZ-BODY ANAEMIA - REPORT OF STUDIES ON 5 PATIENTS WITH MILD ANAEMIA [J].
DACIE, JV ;
STEINGOLD, L ;
MEISLER, A ;
WHITE, JC ;
GRIMES, AJ ;
BEAVEN, GH ;
HEMSTED, EH .
BRITISH JOURNAL OF HAEMATOLOGY, 1964, 10 (03) :388-&
[4]   CHEMICAL STUDIES OF SEVERAL VARIETIES OF HB M [J].
GERALD, PS ;
EFRON, ML .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1961, 47 (11) :1758-+
[6]  
MONN E, 1968, SCAND J HAEMATOL, V5, P353
[7]   HAEMOGLOBIN ZURICH - ALPHA2A BETA263 ARG [J].
MULLER, CJ ;
KINGMA, S .
BIOCHIMICA ET BIOPHYSICA ACTA, 1961, 50 (03) :595-&
[8]  
OPFELL R W, 1968, Journal of Medical Genetics, V5, P292, DOI 10.1136/jmg.5.4.292
[9]   MOLECULAR PATHOLOGY OF HUMAN HAEMOGLOBIN [J].
PERUTZ, MF ;
LEHMANN, H .
NATURE, 1968, 219 (5157) :902-+
[10]   3-DIMENSIONAL FOURIER SYNTHESIS OF HORSE OXYHAEMOGLOBIN AT 2.8 A RESOLUTION - ATOMIC MODEL [J].
PERUTZ, MF ;
MUIRHEAD, H ;
COX, JM ;
GOAMAN, LCG .
NATURE, 1968, 219 (5150) :131-&