CLINICAL AND LABORATORY OBSERVATIONS IN A CHILD WITH HEPATIC PHOSPHORYLASE-KINASE DEFICIENCY

被引：16

作者：

TUCHMAN, M

BROWN, BI

BURKE, BA

ULSTROM, RA

机构：

[1] UNIV MINNESOTA,DEPT LAB MED & PATHOL,MINNEAPOLIS,MN 55455

[2] UNIV MINNESOTA,DEPT BIOL CHEM,MINNEAPOLIS,MN 55455

来源：

METABOLISM-CLINICAL AND EXPERIMENTAL | 1986年 / 35卷 / 07期

关键词：

D O I：

10.1016/0026-0495(86)90169-1

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

页码：627 / 633

页数：7

共 16 条

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OWEN, OE ;

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[5] HEPATIC KETOGENESIS AND GLUCONEOGENESIS IN HUMANS [J].

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[7] PHOSPHORYLASE KINASE OF LIVER - DEFICIENCY IN A GIRL WITH INCREASED HEPATIC GLYCOGEN [J].

HUG, G ;

SCHUBERT, WK ;

CHUCK, G .

SCIENCE, 1966, 153 (3743) :1534-&

[8] DEFICIENT ACTIVITY OF DEPHOSPHOPHOSPHORYLASE KINASE AND ACCUMULATION OF GLYCOGEN IN LIVER [J].

HUG, G ;

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CHUCK, G .

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[9]

HUG G, 1966, AM J DIS CHILD, V3, P457

[10]

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