IDIOPATHIC FEMALE INTERSEX WITH CLITOROMEGALY AND URETHRAL DUPLICATION

被引:11
作者
BELIS, JA [1 ]
HRABOVSKY, EE [1 ]
机构
[1] W VIRGINIA UNIV, MED CTR, DIV PEDIAT SURG, MORGANTOWN, WV 26506 USA
关键词
D O I
10.1016/S0022-5347(17)56614-8
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Idiopathic female intersex presents in the neonate with characteristic anomalies of the external genitalia, complete and separate phallic and vaginal urethras and vesical outlet obstruction. Management of this disorder should initially focus upon adequate urinary drainage and proper sex assignment in the neonate. Successful management and surgical reconstruction of the external genitalia should later result in normal female development.
引用
收藏
页码:805 / 808
页数:4
相关论文
共 20 条
[1]  
BIERICH JR, 1974, HELV PAEDIATR ACTA, P87
[2]  
BLUM V, 1904, MONATSBERICHT J UROL, V9, P522
[3]  
BOISSONNAT P, 1961, Br J Urol, V33, P453
[4]   COMPLETE DUPLICATION OF URETHRA WITH VAGINAL STENOSIS [J].
BONNEY, WW ;
YOUNG, HH ;
LEVIN, D ;
GOODWIN, WE .
JOURNAL OF UROLOGY, 1975, 113 (01) :132-137
[5]   NUCLEAR SEX AND GENITAL MALFORMATION IN 48 CASES OF RENAL AGENESIS, WITH ESPECIAL REFERENCE TO NONSPECIFIC FEMALE PSEUDOHERMAPHRODITISM [J].
CARPENTIER, PJ ;
POTTER, EL .
AMERICAN JOURNAL OF OBSTETRICS AND GYNECOLOGY, 1959, 78 (02) :235-258
[6]  
CLARKE IJ, 1976, J EMBRYOL EXP MORPH, V36, P87
[7]  
Duckett J W Jr, 1974, Urol Clin North Am, V1, P485
[8]   GENETIC AND HORMONAL-CONTROL OF MALE SEXUAL DIFFERENTIATION [J].
GOLDSTEIN, JL ;
WILSON, JD .
JOURNAL OF CELLULAR PHYSIOLOGY, 1975, 85 (02) :365-377
[9]  
GRUBENMANN I, 1912, FRANKFURT Z PATHOL, V10, P101
[10]  
GRUMBACH MM, 1960, FERTIL STERIL, V11, P157