ISCHEMIC OPTIC NEUROPATHY IN A FEMALE CARRIER WITH FABRYS-DISEASE

被引：19

作者：

ABE, H ^{[1
]}

SAKAI, T ^{[1
]}

SAWAGUCHI, S ^{[1
]}

HASEGAWA, S ^{[1
]}

TAKAGI, M ^{[1
]}

YOSHIZAWA, T ^{[1
]}

USUI, T ^{[1
]}

HORIKAWA, Y ^{[1
]}

机构：

[1] SHINRAKUEN HOSP,NEUROL CLIN,NIIGATA,JAPAN

来源：

OPHTHALMOLOGICA | 1992年 / 205卷 / 02期

关键词：

FABRYS DISEASE; WHORL-LIKE CORNEAL DEPOSITS; ISCHEMIC OPTIC NEUROPATHY; CILIORETINAL ARTERY OCCLUSION;

D O I：

10.1159/000310318

中图分类号：

R77 [眼科学];

学科分类号：

100212 ;

摘要：

We report ocular findings of a patient with anterior ischemic optic neuropathy (AION) and cilioretinal artery occlusion in a female carrier of Fabry's disease. Fluorescein angiography revealed delayed filling of the upper and temporal part of peripapillary choroidal vessels and capillaries of the right optic disk and late filling of the cilioretinal artery. CT scanning was performed several times in early stages and demonstrated thickening of the intraorbital optic nerve due to ischemic edema. About 5 months later, the fellow eye showed optic disk edema, an early sign of AION, and was treated by systemic corticosteroid and urokinase whereby AION did not progress.

引用

页码：83 / 88

页数：6

共 11 条

[1]

DESNICK RJ, 1977, METABOLIC BASIS INHE, P810

[2]

FRANCESCHETTI A, 1976, NATIONAL F MARCH DIM, V12, P195

[3] ANTERIOR ISCHEMIC OPTIC NEUROPATHY .5. OPTIC DISK EDEMA AN EARLY SIGN [J].