SANDHOFF DISEASE - DEFECTIVE GLYCOSAMINOGLYCAN CATABOLISM IN CULTURED FIBROBLASTS AND ITS CORRECTION BY BETA-N-ACETYLHEXOSAMINIDASE

被引：56

作者：

CANTZ, M

KRESSE, H

机构：

[1] CHRISTIAN ALBRECHTS UNIV, KINDER KLIN, FROBEL STR 15-17, D-2300 KIEL, WEST GERMANY

[2] WESTFAL WILHELMS UNIV, PHYSIOL CHEM INST, WALDEYER STR 15, D-4400 MUNSTER, WEST GERMANY

来源：

EUROPEAN JOURNAL OF BIOCHEMISTRY | 1974年 / 47卷 / 03期

关键词：

D O I：

10.1111/j.1432-1033.1974.tb03729.x

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：581 / 590

页数：10

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[9] GANGLIOSIDOSIS WITH TOTAL HEXOSAMINIDASE DEFICIENCY - CLINICAL, BIOCHEMICAL AND ULTRASTRUCTURAL STUDIES AND COMPARISON WITH CONVENTIONAL CASES OF TAY-SACHS DISEASE [J].

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[10] DEFECT IN HURLER AND HUNTER SYNDROMES, .2. DEFICIENCY OF SPECIFIC FACTORS INVOLVED IN MUCOPOLYSACCHARIDE DEGRADATION [J].

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