LYSOSOMAL ACID LIPASE IN CULTIVATED FIBROBLASTS - CHARACTERIZATION OF ENZYME-ACTIVITY IN NORMAL AND ENZYMATICALLY DEFICIENT CELL-LINES

被引：34

作者：

BURTON, BK

EMERY, D

MUELLER, HW

机构：

来源：

CLINICA CHIMICA ACTA | 1980年 / 101卷 / 01期

关键词：

D O I：

10.1016/0009-8981(80)90052-2

中图分类号：

R446 [实验室诊断]; R-33 [实验医学、医学实验];

学科分类号：

1001 ;

摘要：

引用

收藏

页码：25 / 32

页数：8

相关论文

共 10 条

[1] CHOLESTEROL ESTER STORAGE DISEASE - CLINICAL, BIOCHEMICAL, AND PATHOLOGICAL-STUDIES
BEAUDET, AL
FERRY, GD
NICHOLS, BL
ROSENBERG, HS
[J]. JOURNAL OF PEDIATRICS, 1977, 90 (06) : 910 - 914
[2] ACID LIPASE ACTIVITY OF HUMAN LYMPHOCYTES
COATES, PM
CORTNER, JA
HOFFMAN, GM
BROWN, SA
[J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1979, 572 (02) : 225 - 234
[3] ACID LIPASE IN CULTURED AMNIOTIC-FLUID CELLS - IMPLICATIONS FOR PRENATAL DIAGNOSIS OF WOLMANS DISEASE
COATES, PM
CORTNER, JA
[J]. PEDIATRIC RESEARCH, 1978, 12 (04) : 450 - 450
[4] GENETIC-VARIATION OF LYSOSOMAL ACID LIPASE
CORTNER, JA
COATES, PM
SWOBODA, E
SCHNATZ, JD
[J]. PEDIATRIC RESEARCH, 1976, 10 (11) : 927 - 932
[5] ACID ESTERASE-ACTIVITY IN CULTURED SKIN FIBROBLASTS AND AMNIOTIC-FLUID CELLS USING 4-METHYLUMBELLIFERYL PALMITATE
GUY, GJ
BUTTERWORTH, J
[J]. CLINICA CHIMICA ACTA, 1978, 84 (03) : 361 - 371
[6] WOLMANS DISEASE . DEFICIENCY OF E600-RESISTANT ACID ESTERASE ACTIVITY WITH STORAGE OF LIPIDS IN LYSOSOMES
LAKE, BD
PATRICK, AD
[J]. JOURNAL OF PEDIATRICS, 1970, 76 (02) : 262 - +
[7] The determination of enzyme dissociation constants
Lineweaver, H
Burk, D
[J]. JOURNAL OF THE AMERICAN CHEMICAL SOCIETY, 1934, 56 : 658 - 666
[8] Patrick A D, 1969, Nature, V222, P1067, DOI 10.1038/2221067a0
[9] SCHOTZ MC, 1970, J LIPID RES, V11, P68
[10] ENZYME DEFICIENCY IN CHOLESTERYL ESTER STORAGE-DISEASE
SLOAN, HR
FREDRICKSON, DS
[J]. JOURNAL OF CLINICAL INVESTIGATION, 1972, 51 (07) : 1923 - +