BRANCHED-CHAIN ALPHA-KETO ACIDS ISOLATED AS OXIME DERIVATIVES - RELATIONSHIP TO CORRESPONDING HYDROXY-ACIDS AND AMINO-ACIDS IN MAPLE SYRUP URINE DISEASE

被引：49

作者：

LANCASTER, G

MAMER, OA

SCRIVER, CR

机构：

[1] ROY VICTORIA HOSP, DEPT MED, MASS SPECTR, MONTREAL, QUEBEC, CANADA

[2] MCGILL UNIV, MONTREAL CHILDRENS HOSP,RES INST,DEPT PEDIAT, DEBELLE LAB BIOCHEM GENET,2300 TUPPER, MONTREAL 108, QUEBEC, CANADA

来源：

METABOLISM-CLINICAL AND EXPERIMENTAL | 1974年 / 23卷 / 03期

关键词：

D O I：

10.1016/0026-0495(74)90064-X

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

引用

收藏

页码：257 / 265

页数：9

相关论文

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