INCREASED AMMONIA PRODUCTION DURING FOREARM ISCHEMIC WORK TEST IN MCARDLES DISEASE

被引:31
作者
RUMPF, KW [1 ]
WAGNER, H [1 ]
KAISER, H [1 ]
MEINCK, HM [1 ]
GOEBEL, HH [1 ]
SCHELER, F [1 ]
机构
[1] UNIV GOTTINGEN,NEUROL KLIN,NEUROPHYS & NEUROPATHOL ABT,D-3400 GOTTINGEN,FED REP GER
来源
KLINISCHE WOCHENSCHRIFT | 1981年 / 59卷 / 23期
关键词
D O I
10.1007/BF01711182
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1319 / 1320
页数:2
相关论文
共 11 条
[1]  
DIMAURO S, 1979, HDB CLIN NEUROLOGY, V41, P185
[2]  
Dubowitz V., 1973, MUSCLE BIOPSY MODERN
[3]   MYOADENYLATE DEAMINASE DEFICIENCY - NEW DISEASE OF MUSCLE [J].
FISHBEIN, WN ;
ARMBRUSTMACHER, VW ;
GRIFFIN, JL .
SCIENCE, 1978, 200 (4341) :545-548
[4]  
GUTMANN I, 1974, METHODEN ENZYMATISCH, V2, P1510
[5]   AMMONIA PRODUCTION IN MUSCLE AND OTHER TISSUES - PURINE NUCLEOTIDE CYCLE [J].
LOWENSTEIN, JM .
PHYSIOLOGICAL REVIEWS, 1972, 52 (02) :382-+
[6]  
MCARDLE B, 1951, CLIN SCI, V10, P13
[7]   A METABOLIC MYOPATHY DUE TO ABSENCE OF MUSCLE PHOSPHORYLASE [J].
PEARSON, CM ;
MOMMAERTS, WFH ;
RIMER, DG .
AMERICAN JOURNAL OF MEDICINE, 1961, 30 (04) :502-&
[8]  
PERNOW BB, 1967, ACTA MED SCAND S, V427, P294
[9]   DISRUPTION OF THE PURINE NUCLEOTIDE CYCLE - A POTENTIAL EXPLANATION FOR MUSCLE DYSFUNCTION IN MYOADENYLATE DEAMINASE DEFICIENCY [J].
SABINA, RL ;
SWAIN, JL ;
PATTEN, BM ;
ASHIZAWA, T ;
OBRIEN, WE ;
HOLMES, EW .
JOURNAL OF CLINICAL INVESTIGATION, 1980, 66 (06) :1419-1423
[10]   KINETIC DETERMINATION OF AMMONIA IN PLASMA [J].
VANANKEN, HC ;
SCHIPHORST, ME .
CLINICA CHIMICA ACTA, 1974, 56 (02) :151-157