MUCOLIPIDOSIS-1 - INCREASED SIALIC-ACID CONTENT AND DEFICIENCY OF ANALPHA-N-ACETYLNEURAMINIDASE IN CULTURED FIBROBLASTS

被引:143
作者
CANTZ, M [1 ]
GEHLER, J [1 ]
SPRANGER, J [1 ]
机构
[1] UNIV MAINZ,DEPT PEDIAT,D-6500 MAINZ,FED REP GER
关键词
D O I
10.1016/0006-291X(77)90363-1
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:732 / 738
页数:7
相关论文
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