PELIZAEUS-MERZBACHER DISEASE - BRAIN LIPID AND FATTY-ACID COMPOSITION

被引:21
作者
BOURRE, JM
BORNHOFEN, JH
ARAOZ, CA
DAUDU, O
BAUMANN, NA
机构
[1] UNIV ARKANSAS,DEPT PEDIAT,LITTLE ROCK,AR 72201
[2] UNIV ARKANSAS,DEPT NEUROL,LITTLE ROCK,AR 72201
关键词
D O I
10.1111/j.1471-4159.1978.tb10777.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:719 / 727
页数:9
相关论文
共 56 条
  • [1] Allegranza A, 1968, Acta Neurol (Napoli), V23, P895
  • [2] BARTLETT GR, 1959, J BIOL CHEM, V234, P466
  • [3] FATTY ACID AND LIPID COMPOSITION OF BRAIN OF A MYELIN DEFICIENT MUTANT QUAKING MOUSE
    BAUMANN, NA
    JACQUE, CM
    POLLET, SA
    HARPIN, ML
    [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1968, 4 (03): : 340 - &
  • [4] Bielschowsky M, 1928, J PSYCHOL NEUROL, V36, P131
  • [5] The issue of the Pelizaeus-Merzbacher disease
    Bodechtel, G
    [J]. ZEITSCHRIFT FUR DIE GESAMTE NEUROLOGIE UND PSYCHIATRIE, 1929, 121 : 487 - 507
  • [6] BONHOFF G, 1957, HDB SPEZIELLEN PATHO, P716
  • [7] BOSTROEM A., 1927, DEUTSCHE ZEITSCHR NERVENHEILK, V100, P63, DOI 10.1007/BF01993178
  • [8] NERVONIC ACID BIOSYNTHESIS BY ERUCYL-COA ELONGATION IN NORMAL AND QUAKING MOUSE-BRAIN MICROSOMES - ELONGATION OF OTHER UNSATURATED FATTY ACYL-COAS (MONO AND POLY-UNSATURATED)
    BOURRE, JM
    DAUDU, O
    BAUMANN, N
    [J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1976, 424 (01) : 1 - 7
  • [9] ONTOGENESIS OF 3 FATTY-ACID SYNTHESIZING SYSTEMS IN CEREBRAL MICROSOMES IN RELATION WITH MYELINATION
    BOURRE, JM
    DAUDU, O
    BAUMANN, N
    [J]. BIOCHIMIE, 1976, 58 (10) : 1277 - 1279
  • [10] LIGNOCERIC ACID BIOSYNTHESIS IN DEVELOPING BRAIN - ACTIVITIES OF MITOCHONDRIAL ACETYL-COA-DEPENDENT SYNTHESIS AND MICROSOMAL MALONYL-COA CHAIN-ELONGATING SYSTEM IN RELATION TO MYELINATION - COMPARISON BETWEEN NORMAL MOUSE AND DYSMYELINATING MUTANTS (QUAKING AND JIMPY)
    BOURRE, JM
    PATURNEAUJOUAS, MY
    DAUDU, OL
    BAUMANN, NA
    [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1977, 72 (01): : 41 - 47