EXCRETION OF CHONDROITIN SULFATE C WITH LOW SULFATE CONTENT BY PATIENTS WITH GENERALIZED PLATYSPONDYLY (BRACHYOLMIA)

被引:35
作者
MOURAO, PAS [1 ]
TOLEDO, SPA [1 ]
NADER, HB [1 ]
DIETRICH, CP [1 ]
机构
[1] ESCOLA PAULISTA MED,DEPT BIOQUIM & FARMACOL,SAO PAULO,BRAZIL
来源
BIOCHEMICAL MEDICINE | 1973年 / 7卷 / 03期
关键词
D O I
10.1016/0006-2944(73)90062-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:415 / 423
页数:9
相关论文
共 19 条
[1]   HURLER SYNDROME - A BIOCHEMICAL AND CLINICAL STUDY [J].
BERGGARD, I ;
BEARN, AG .
AMERICAN JOURNAL OF MEDICINE, 1965, 39 (02) :221-&
[2]  
DAVES S, 1969, AM J MED, V47, P708
[3]   CHEMICAL COMPOSITION OF HEPARITIN SULFATE - FRACTIONATION AND CHARACTERIZATION OF 4 ACIDIC MUCOPOLYSACCHARIDES IN HEPARITIN SULFATE FROM BEEF LUNG TISSUE [J].
DIETRICH, CP ;
NADER, HB ;
BRITTO, LRG ;
SILVA, ME .
BIOCHIMICA ET BIOPHYSICA ACTA, 1971, 237 (03) :430-&
[4]   SIMPLE MICRO METHOD FOR IDENTIFICATION OF HEPARIN AND OTHER ACIDIC MUCOPOLYSACCHARIDES FROM MAMMALIAN TISSUES [J].
DIETRICH, CP ;
DIETRICH, SM .
ANALYTICAL BIOCHEMISTRY, 1972, 46 (01) :209-&
[5]   ENZYMIC DEGRADATION OF HEPARIN . A GLUCOSAMINIDASE AND A GLYCURONIDASE FROM FLAVOBACTERIUM HEPARINUM [J].
DIETRICH, CP .
BIOCHEMISTRY, 1969, 8 (05) :2089-&
[6]  
DIETRICH CP, IN PRESS
[7]  
DIETRICH CP, 1972, BIOCHEMISTRY GLYCOSI, V2
[8]  
DISCHE Z, 1947, J BIOL CHEM, V167, P189
[9]   HURLER AND HUNTER SYNDROMES [J].
DORFMAN, A ;
MATALON, R .
AMERICAN JOURNAL OF MEDICINE, 1969, 47 (05) :691-&
[10]  
GLICK D, 1958, METHODS BIOCHEMIC ED, V6, P289