METABOLISM OF L-PYROGLUTAMIC ACID IN FIBROBLASTS FROM A PATIENT WITH PYROGLUTAMIC ACIDURIA - DEMONSTRATION OF AN L-PYROGLUTAMATE HYDROLASE SYSTEM

被引:25
作者
STROMME, JH
ELDJARN, L
机构
关键词
D O I
10.3109/00365517209080249
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:335 / &
相关论文
共 15 条
[1]   ACIDIC PEPTIDES OF LENS .6. METABOLISM OF GAMMA-GLUTAMYL PEPTIDES IN SUBCELLULAR FRACTIONS OF RABBIT LIVER [J].
CLIFFE, EE ;
WALEY, SG .
BIOCHEMICAL JOURNAL, 1961, 79 (01) :118-&
[2]   ENZYMIC FORMATION OF PYRROLIDONE CARBOXYLIC ACID FROM GAMMA-GLUTAMYL PEPTIDES [J].
CONNELL, GE ;
HANES, CS .
NATURE, 1956, 177 (4504) :377-378
[3]  
ELDJARN L, 1971, 9 SSIEM S LEEDS
[4]  
ELDJARN L, IN PRESS
[5]  
FODOR PJ, 1953, J BIOL CHEM, V202, P551
[6]  
HSIA DYY, 1970, CLIN GENET, V1, P5
[7]   PYROGLUTAMIC ACIDURIA - A NEW INBORN ERROR OF METABOLISM [J].
JELLUM, E ;
KLUGE, T ;
BORRESEN, HC ;
STOKKE, O ;
ELDJARN, L .
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION, 1970, 26 (04) :327-&
[8]  
KLUGE T, 1972, SURGERY, V71, P104
[9]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[10]  
MEISTER A, PERSONAL COMMUNICATI