SERUM CARNITINE LEVEL IN PHENYLKETONURIC CHILDREN UNDER DIETARY CONTROL IN GREECE

被引：28

作者：

SCHULPIS, KH ^{[1
]}

NOUNOPOULOS, C ^{[1
]}

SCARPALEZOU, A ^{[1
]}

BOULOUKOS, A ^{[1
]}

MISSIOUTSAGARAKIS, S ^{[1
]}

机构：

[1] UNIV ATHENS, SCH MED, DEPT BIOCHEM, ATHENS, GREECE

来源：

ACTA PAEDIATRICA SCANDINAVICA | 1990年 / 79卷 / 10期

关键词：

Carnitine; Phenylketonuria; Vegetarian diet;

D O I：

10.1111/j.1651-2227.1990.tb11354.x

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Although total, free and esterified carnitine blood levels were found to be low (p < 0.001) in phenylketonuric patients under dietary treatment compared to controls, no clinical signs of carnitine deficiency were noticed. Exclusion from the PKU diet of nutrients rich in carnitine has been suggested. Supplementation of the diets with carnitine or preferably enrichment of the PKU formulas with carcnitine will rectify the restriction of extrinsic carnitine in PKU dietary treatment.

引用

页码：930 / 934

页数：5

共 24 条

[1] ROLE OF THE LIVER IN THE PATHOGENESIS OF CEREBRAL-DISORDERS IN PHENYLKETONURIA [J].