MITRAL-VALVE PROLAPSE - A CONSISTENT MANIFESTATION OF TYPE-IV EHLERS-DANLOS SYNDROME - THE PATHOGENETIC ROLE OF THE ABNORMAL PRODUCTION OF TYPE-III COLLAGEN

被引:94
作者
JAFFE, AS
GELTMAN, EM
RODEY, GE
UITTO, J
机构
[1] WASHINGTON UNIV,SCH MED,DEPT MED,DIV DERMATOL,ST LOUIS,MO 63110
[2] WASHINGTON UNIV,SCH MED,DEPT LAB MED,ST LOUIS,MO 63110
关键词
D O I
10.1161/01.CIR.64.1.121
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:121 / 125
页数:5
相关论文
共 16 条
[1]   COLLAGEN IN CUTANEOUS DISEASES [J].
BAUER, EA ;
UITTO, J .
INTERNATIONAL JOURNAL OF DERMATOLOGY, 1979, 18 (04) :251-270
[2]   COLLAGEN BIOSYNTHESIS BY HUMAN-SKIN FIBROBLASTS .1. OPTIMIZATION OF THE CULTURE CONDITIONS FOR SYNTHESIS OF TYPE-I AND TYPE-III PROCOLLAGENS [J].
BOOTH, BA ;
POLAK, KL ;
UITTO, J .
BIOCHIMICA ET BIOPHYSICA ACTA, 1980, 607 (01) :145-160
[3]  
BRAUN WE, 1977, TRANSPLANT P, V9, P1869
[4]   CLINICAL AND ULTRASTRUCTURAL HETEROGENEITY OF TYPE-IV EHLERS-DANLOS SYNDROME [J].
BYERS, PH ;
HOLBROOK, KA ;
MCGILLIVRAY, B ;
MACLEOD, PM ;
LOWRY, RB .
HUMAN GENETICS, 1979, 47 (02) :141-150
[5]   PREVALENCE OF MITRAL-VALVE PROLAPSE IN PRESUMABLY HEALTHY-YOUNG MEN [J].
DARSEE, JR ;
MIKOLICH, JR ;
NICOLOFF, NB ;
LESSER, LE .
CIRCULATION, 1979, 59 (04) :619-622
[6]  
DAVIES MJ, 1978, BRIT HEART J, V40, P468
[7]  
FEIGENBAUM H, 1976, ECHOCARDIOGR-J CARD, P119
[8]   MITRAL-VALVE PROLAPSE - 2-DIMENSIONAL ECHOCARDIOGRAPHIC AND ANGIOGRAPHIC CORRELATION [J].
GILBERT, BW ;
SCHATZ, RA ;
VONRAMM, OT ;
BEHAR, VS ;
KISSLO, JA .
CIRCULATION, 1976, 54 (05) :716-729
[9]   ALTERED COLLAGEN COMPOSITION IN A PROLAPSING MITRAL-VALVE WITH RUPTURED CHORDAE TENDINEAE [J].
HAMMER, D ;
LEIER, CV ;
BABA, N ;
VASKO, JS ;
WOOLEY, CF ;
PINNELL, SR .
AMERICAN JOURNAL OF MEDICINE, 1979, 67 (05) :863-866
[10]  
JERASATY RM, 1979, MITRAL VALVE PROLAPS