POLYCYSTIC KIDNEYS ASSOCIATED WITH MARFAN-SYNDROME IN AN ADULT

被引:8
作者
BIERMANN, CW [1 ]
RUTISHAUSER, G [1 ]
机构
[1] UNIV BASEL,DEPT UROL,BASEL,SWITZERLAND
来源
SCANDINAVIAN JOURNAL OF UROLOGY AND NEPHROLOGY | 1994年 / 28卷 / 03期
关键词
MARFAN SYNDROME; POLYCYSTIC KIDNEYS; SIMULTANEOUS HEREDITARY DISEASE;
D O I
10.3109/00365599409181282
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
A 41-year-old man with Marfan syndrome was found to have polycystic renal disease and underwent emergency surgery for dissecting aneurysm of the ascending aorta. To our knowledge only two cases of this rare combination of hereditary disorders have been described in the literature.
引用
收藏
页码:295 / 296
页数:2
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