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DEFICIENT HEXOSAMINIDASE ACTIVITY IN AN EXCEPTIONAL CASE OF TAY-SACHS DISEASE WITH ADDITIONAL STORAGE OF KIDNEY GLOBOSIDE IN VISCERAL ORGANS
被引:241
作者
:
SANDHOFF, K
论文数:
0
引用数:
0
h-index:
0
SANDHOFF, K
ANDREAE, U
论文数:
0
引用数:
0
h-index:
0
ANDREAE, U
JATZKEWITZ, H
论文数:
0
引用数:
0
h-index:
0
JATZKEWITZ, H
机构
:
来源
:
LIFE SCIENCES PART 1 PHYSIOLOGY AND PHARMACOLOGY AND PART 2 BIOCHEMISTRY GENERAL AND MOLECULAR BIOLOGY
|
1968年
/ 7卷
/ 6P2期
关键词
:
D O I
:
10.1016/0024-3205(68)90024-6
中图分类号
:
Q [生物科学];
学科分类号
:
07 ;
0710 ;
09 ;
摘要
:
引用
收藏
页码:283 / +
页数:1
相关论文
共 8 条
[1]
INHIBITION OF GLYCOSIDASES BY ALDONOLACTONES OF CORRESPONDING CONFIGURATION .2. INHIBITORS OF BETA-N-ACETYLGLUCOSAMINIDASE
FINDLAY, J
论文数:
0
引用数:
0
h-index:
0
FINDLAY, J
LEVVY, GA
论文数:
0
引用数:
0
h-index:
0
LEVVY, GA
MARSH, CA
论文数:
0
引用数:
0
h-index:
0
MARSH, CA
[J].
BIOCHEMICAL JOURNAL,
1958,
69
: 467
-
476
[2]
ON A BIOCHEMICALLY SPECIAL FORM OF INFANTILE AMAUROTIC IDIOCY
JATZKEWITZ, H
论文数:
0
引用数:
0
h-index:
0
JATZKEWITZ, H
SANDHOFF, K
论文数:
0
引用数:
0
h-index:
0
SANDHOFF, K
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1963,
70
(03)
: 354
-
&
[3]
Klenk E., 1939, Z PHYSIOL CHEM, V262, P128
[4]
LEABACK DH, 1963, BIOCHEM PREP, V10, P118
[5]
MAKITA A, 1964, J BIOCHEM-TOKYO, V55, P202
[6]
SANDHOFF K, 1965, THESIS U MUNCHEN
[7]
CHEMICAL STRUCTURE OF NORMAL HUMAN BRAIN AND TAY-SACHS GANGLIOSIDES
SVENNERHOLM, L
论文数:
0
引用数:
0
h-index:
0
SVENNERHOLM, L
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1962,
9
(05)
: 436
-
&
[8]
WABLE W, 1967, THESIS U MUNCHEN
←
1
→
共 8 条
[1]
INHIBITION OF GLYCOSIDASES BY ALDONOLACTONES OF CORRESPONDING CONFIGURATION .2. INHIBITORS OF BETA-N-ACETYLGLUCOSAMINIDASE
FINDLAY, J
论文数:
0
引用数:
0
h-index:
0
FINDLAY, J
LEVVY, GA
论文数:
0
引用数:
0
h-index:
0
LEVVY, GA
MARSH, CA
论文数:
0
引用数:
0
h-index:
0
MARSH, CA
[J].
BIOCHEMICAL JOURNAL,
1958,
69
: 467
-
476
[2]
ON A BIOCHEMICALLY SPECIAL FORM OF INFANTILE AMAUROTIC IDIOCY
JATZKEWITZ, H
论文数:
0
引用数:
0
h-index:
0
JATZKEWITZ, H
SANDHOFF, K
论文数:
0
引用数:
0
h-index:
0
SANDHOFF, K
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1963,
70
(03)
: 354
-
&
[3]
Klenk E., 1939, Z PHYSIOL CHEM, V262, P128
[4]
LEABACK DH, 1963, BIOCHEM PREP, V10, P118
[5]
MAKITA A, 1964, J BIOCHEM-TOKYO, V55, P202
[6]
SANDHOFF K, 1965, THESIS U MUNCHEN
[7]
CHEMICAL STRUCTURE OF NORMAL HUMAN BRAIN AND TAY-SACHS GANGLIOSIDES
SVENNERHOLM, L
论文数:
0
引用数:
0
h-index:
0
SVENNERHOLM, L
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1962,
9
(05)
: 436
-
&
[8]
WABLE W, 1967, THESIS U MUNCHEN
←
1
→