INHIBITION OF GLYCINE OXIDATION IN CULTURED FIBROBLASTS BY ISOLEUCINE

被引:18
作者
HILLMAN, RE [1 ]
SOWERS, LH [1 ]
COHEN, JL [1 ]
机构
[1] WASHINGTON UNIV,ST LOUIS CHILDRENS HOSP,SCH MED,DEPT PEDIAT,DIV ED GENET,ST LOUIS,MO 63110
关键词
D O I
10.1203/00006450-197312000-00001
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:945 / 947
页数:3
相关论文
共 8 条
[1]   ISOVALERIC ACIDEMIA PRESENTING WITH ALTERED METABOLISM OF GLYCINE [J].
ANDO, T ;
KLINGBERG, WG ;
WARD, AN ;
RASMUSSEN, K ;
NYHAN, WL .
PEDIATRIC RESEARCH, 1971, 5 (09) :478-+
[2]  
CHILDS B, 1961, PEDIATRICS, V27, P522
[3]  
HILLMAN RS, IN PRESS
[4]  
HSIA YE, 1969, LANCET, V1, P757
[5]  
KEATING JP, 1972, PEDIATRICS, V50, P890
[7]   TIGLICACIDURIA IN PROPIONICACIDEMIA [J].
NYHAN, WL ;
ANDO, T ;
COTTOM, D ;
WADLINGTON, W ;
RASMUSSEN, K ;
HULL, D ;
KILROY, AW .
BIOCHEMICAL JOURNAL, 1972, 126 (04) :1035-+
[8]   METHYLMALONIC ACIDURIA - AN INBORN ERROR LEADING TO METABOLIC ACIDOSIS LONG-CHAIN KETONURIA AND INTERMITTENT HYPERGLYCINEMIA [J].
ROSENBERG, LE ;
LILLEQVI.AC ;
HSIA, YE .
NEW ENGLAND JOURNAL OF MEDICINE, 1968, 278 (24) :1319-+