LABAND SYNDROME - REPORT OF 2 CASES, REVIEW OF THE LITERATURE, AND IDENTIFICATION OF ADDITIONAL MANIFESTATIONS

被引:22
作者
CHADWICK, B [1 ]
HUNTER, B [1 ]
HUNTER, L [1 ]
ALDRED, M [1 ]
WILKIE, A [1 ]
机构
[1] UNIV QUEENSLAND,ST LUCIA,QLD 4067,AUSTRALIA
来源
ORAL SURGERY ORAL MEDICINE ORAL PATHOLOGY ORAL RADIOLOGY AND ENDODONTICS | 1994年 / 78卷 / 01期
关键词
D O I
10.1016/0030-4220(94)90118-X
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
Twenty-six persons with Laband syndrome have been reported in the literature to date. We report two further unrelated cases and suggest that a skeletal anterior open bite and symmetric soft tissue swelling of the vault of the palate be added to the variable features associated with the syndrome. There is clear evidence in the literature of autosomal dominant inheritance but our analysis indicates that in some cases recessive transmission is likely.
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页码:57 / 63
页数:7
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