ANGIOOSTEOHYPERTROPHY SYNDROME WITH PROTEIN-LOSING ENTEROPATHY

被引:5
作者
CAPLAN, DB
HERSKOVIC, T
GRYBOSKI, JD
机构
[1] Department of Pediatrics, Yale University School of Medicine, New Haven, CT
[2] Department ofMedicine, Yale University School of Medicine, New Haven, CT
关键词
D O I
10.1016/S0022-3476(69)80019-3
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A child with the characteristic features ofthe angioosteohypertrophy syndrome and evidence of protein-losing enteropathy is presented. Studies indicate that intestinal lymphangiectasia was responsible for the gastrointestinal losses of protein and fat. A diet low in long-chain triglycerides and supplemented by medium-chain triglycerides effectively reversed the enteric losses. © 1969 The C. V. Mosby Company.
引用
收藏
页码:119 / +
页数:1
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