CLINICAL AND NEUROPATHOLOGIC ASSESSMENT OF SEVERITY IN HUNTINGTONS-DISEASE

被引:172
作者
MYERS, RH
VONSATTEL, JP
STEVENS, TJ
CUPPLES, LA
RICHARDSON, EP
MARTIN, JB
BIRD, ED
机构
[1] HARVARD UNIV,MASSACHUSETTS GEN HOSP,SCH MED,JAMES HOMER WRIGHT PATHOL LABS,BOSTON,MA 02114
[2] HARVARD UNIV,SCH MED,DEPT NEUROL NEUROPATHOL,BOSTON,MA 02115
[3] MCLEAN HOSP,MAILMAN RES CTR,RALPH LOWELL LABS,BELMONT,MA 02178
[4] HARVARD UNIV,SCH MED,BELMONT,MA 02178
[5] BOSTON UNIV,SCH PUBL HLTH,BOSTON,MA 02215
[6] HARVARD UNIV,MASSACHUSETTS GEN HOSP,SCH MED,DEPT NEUROL,BOSTON,MA 02114
关键词
D O I
10.1212/WNL.38.3.341
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:341 / 347
页数:7
相关论文
共 26 条
[1]   SEX RELATED FACTOR IN INHERITANCE OF HUNTINGTONS-CHOREA [J].
BIRD, ED ;
CARO, AJ ;
PILLING, JB .
ANNALS OF HUMAN GENETICS, 1974, 37 (JAN) :255-260
[2]   RELATION OF SEX OF AFFECTED PARENT TO AGE AT ONSET OF HUNTINGTONS DISEASE [J].
BRACKENRIDGE, CJ .
JOURNAL OF MEDICAL GENETICS, 1973, 10 (04) :333-336
[3]   COMPARISON OF NEUROPSYCHOLOGICAL DEFICITS ASSOCIATED WITH EARLY AND ADVANCED HUNTINGTONS-DISEASE [J].
BUTTERS, N ;
SAX, D ;
MONTGOMERY, K ;
TARLOW, S .
ARCHIVES OF NEUROLOGY, 1978, 35 (09) :585-589
[4]  
CAINE ED, 1983, AM J PSYCHIAT, V140, P728
[5]  
CONNEALLY P M, 1984, Genetic Epidemiology, V1, P81, DOI 10.1002/gepi.1370010110
[6]  
CONNEALLY PM, 1984, AM J HUM GENET, V36, P506
[7]   PROGRESSION RATE AND AGE AT ONSET ARE RELATED IN AUTOSOMAL DOMINANT NEUROLOGIC DISEASES [J].
CURRIER, RD ;
JACKSON, JF ;
MEYDRECH, EF .
NEUROLOGY, 1982, 32 (08) :907-909
[8]  
Davison C, 1932, ARCH NEUROL PSYCHIAT, V27, P906
[9]   Pathologic changes in Huntington's chorea with special reference to the corpus striatum [J].
Dunlap, CB .
ARCHIVES OF NEUROLOGY AND PSYCHIATRY, 1927, 18 (06) :867-943
[10]  
FARRER LA, 1985, AM J HUM GENET, V37, P350