CYTOPLASMIC INCLUSIONS IN JUVENILE AMAUROTIC IDIOCY

被引：32

作者：

GONATAS, NK

GAMBETTI, P

TUCKER, SH

EVANGELISTA, I

BAIRD, HW

机构：

[1] Department of Pathology (Neuropathology), the University of Pennsylvania School of Medicine, Children's Hospital, Philadelphia, PA

[2] Department of Neurology, the University of Pennsylvania School of Medicine, Children's Hospital, Philadelphia, PA

[3] Department of Pediatrics, the University of Pennsylvania School of Medicine, Children's Hospital, Philadelphia, PA

[4] St. Christopher's Hospital for Children, Philadelphia, PA

[5] Department of Pediatrics, Temple University Health Center, School of Medicine, Philadelphia, PA

来源：

JOURNAL OF PEDIATRICS | 1969年 / 75卷 / 05期

关键词：

D O I：

10.1016/S0022-3476(69)80302-1

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Several forms of neuronal and glial cytoplasmic bodies have been observed with the electron microscope in cerebral biopsies from patients with juvenile amaurotic idiocy. In this study, another cytoplasmic inclusion, with contents resembling fingerprint markings,8 has been found in neurons and astrocytes in 4 cases of juvenile amaurotic idiocy. These studie suggest that juvenile amaurotic idiocy is the manifestation of several distinct cellular disorders. © 1969 The C. V. Mosby Company.

引用

页码：796 / +

页数：1

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