CYSTINOSIS - THERAPEUTIC IMPLICATIONS OF IN-VITRO STUDIES OF CULTURED FIBROBLASTS

被引:16
作者
SCHULMAN, JD
BRADLEY, KH
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D O I
10.1016/S0022-3476(71)80355-4
中图分类号
R72 [儿科学];
学科分类号
100202 ;
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页码:833 / +
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共 26 条
[1]  
BAUER B, 1966, HELV PAEDIATR ACTA, V21, P19
[2]  
BERGER H, 1964, ANN PAEDIATR-BASEL, V202, P465
[3]  
BICKEL H, 1952, ACTA PAEDIATR SC S90, V42, P27
[4]  
CLAYTON BE, 1961, LANCET, V2, P909
[5]   CYSTINOSIS - PLASMA CYSTINE AND CYSTEINE CONCENTRATIONS AND EFFECT OF D-PENICILLAMINE AND DIETARY TREATMENT [J].
CRAWHALL, JC ;
LIETMAN, PS ;
SCHNEIDER, JA ;
SEEGMILLER, JE .
AMERICAN JOURNAL OF MEDICINE, 1968, 44 (03) :330-+
[6]   SEPARATION OF CYSTINE PENICILLAMINE DISULFIDE AND CYSTEINE-PENICILLAMINE MIXED DISULFIDE BY AUTOMATIC AMINO ACID ANALYSIS [J].
CRAWHALL, JC ;
THOMPSON, CJ ;
BRADLEY, KH .
ANALYTICAL BIOCHEMISTRY, 1966, 14 (03) :405-+
[7]  
GOLDMAN H, 1970, LANCET, V1, P811
[8]   PENICILLAMINE TREATMENT OF CYSTINOSIS [J].
HAMBRAEUS, L ;
BROBERGER, O .
ACTA PAEDIATRICA SCANDINAVICA, 1967, 56 (03) :243-+
[9]   HUMAN CYSTINOSIS - INTRACELLULAR DEPOSITION OF CYSTINE [J].
HUMMELER, K ;
ZAJAC, BA ;
GENEL, M ;
HOLTZAPPLE, PG ;
SEGAL, S .
SCIENCE, 1970, 168 (3933) :859-+