GANGLIOSIDE GM3 SIALIDASE ACTIVITY IN FIBROBLASTS OF NORMAL INDIVIDUALS AND OF PATIENTS WITH SIALIDOSIS AND MUCOLIPIDOSIS-IV - SUBCELLULAR-DISTRIBUTION AND SOME PROPERTIES

被引:35
作者
LIESER, M
HARMS, E
KERN, H
BACH, G
CANTZ, M
机构
[1] UNIV HEIDELBERG,INST PATHOCHEM & GEN NEUROCHEM,NEUENHEIMER FELD 220,D-6900 HEIDELBERG,FED REP GER
[2] UNIV MUNSTER,DEPT PEDIAT,D-4400 MUNSTER,FED REP GER
[3] EUROPEAN MOLEC BIOL LAB,D-6900 HEIDELBERG,FED REP GER
[4] HEBREW UNIV JERUSALEM,HADASSAH MED CTR,DEPT HUMAN GENET,JERUSALEM,ISRAEL
关键词
D O I
10.1042/bj2600069
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
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页码:69 / 74
页数:6
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