INTRACRANIAL PLASMA-CELL GRANULOMA PRESENTING AS AN OPTIC NEUROPATHY

被引:10
作者
KODSI, SR
YOUNGE, BR
LEAVITT, JA
CAMPBELL, RJ
SCHEITHAUER, BW
机构
[1] MAYO CLIN & MAYO FDN,DEPT OPHTHALMOL,200 1ST ST SW,ROCHESTER,MN 55905
[2] MAYO CLIN & MAYO FDN,SURG PATHOL SECT,ROCHESTER,MN 55905
关键词
INTRACRANIAL PLASMA CELL GRANULOMA; MAGNETIC RESONANCE IMAGING; OPTIC NEUROPATHY; TRIGEMINAL NERVE; STEROIDS;
D O I
10.1016/0039-6257(93)90056-D
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
A 40-year-old man presented with a left optic neuropathy. Magnetic resonance imaging demonstrated a contrast-enhancing mass along the course of the left trigeminal nerve and in the region of the left cavernous sinus with suprasellar extension. Preoperatively, he had a serum polyclonal gammopathy. Pathologic diagnosis was an intracranial plasma cell granuloma. The patient responded to high-dose steroids with resolution of his optic neuropathy, marked decrease in the size of the mass, and resolution of the serum polyclonal gammopathy. Intracranial plasma cell granuloma is a rare lesion; only 11 cases have been described in the literature. Almost half of the patients presented with vision loss as their chief complaint.
引用
收藏
页码:70 / 74
页数:5
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