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ADRENOLEUKODYSTROPHY
被引:48
作者
:
MOSER, HW
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,BALTIMORE,MD 21205
MOSER, HW
[
1
]
BERGIN, A
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,BALTIMORE,MD 21205
BERGIN, A
[
1
]
NAIDU, S
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,BALTIMORE,MD 21205
NAIDU, S
[
1
]
LADENSON, PW
论文数:
0
引用数:
0
h-index:
0
机构:
JOHNS HOPKINS UNIV,SCH MED,BALTIMORE,MD 21205
JOHNS HOPKINS UNIV,SCH MED,BALTIMORE,MD 21205
LADENSON, PW
[
1
]
机构
:
[1]
JOHNS HOPKINS UNIV,SCH MED,BALTIMORE,MD 21205
来源
:
ENDOCRINOLOGY AND METABOLISM CLINICS OF NORTH AMERICA
|
1991年
/ 20卷
/ 02期
关键词
:
D O I
:
10.1016/S0889-8529(18)30270-6
中图分类号
:
R5 [内科学];
学科分类号
:
1002 ;
100201 ;
摘要
:
引用
收藏
页码:297 / 318
页数:22
相关论文
共 73 条
[1]
AUBOURG P, 1990, AM J HUM GENET, V46, P459
[2]
MRI DETECTS CEREBRAL INVOLVEMENT IN NEUROLOGICALLY ASYMPTOMATIC PATIENTS WITH ADRENOLEUKODYSTROPHY
AUBOURG, P
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
AUBOURG, P
SELLIER, N
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
SELLIER, N
CHAUSSAIN, JL
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
CHAUSSAIN, JL
KALIFA, G
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
KALIFA, G
[J].
NEUROLOGY,
1989,
39
(12)
: 1619
-
1621
[3]
ADRENOLEUKODYSTROPHY - ITS DIVERSE CT APPEARANCES AND AN EVOLUTIVE OR PHENOTYPIC VARIANT - THE LEUKODYSTROPHY WITHOUT ADRENAL INSUFFICIENCY
AUBOURG, P
论文数:
0
引用数:
0
h-index:
0
机构:
FOCH HOSP,DEPT NEURORADIOL,F-92150 SURESNES,FRANCE
AUBOURG, P
DIEBLER, C
论文数:
0
引用数:
0
h-index:
0
机构:
FOCH HOSP,DEPT NEURORADIOL,F-92150 SURESNES,FRANCE
DIEBLER, C
[J].
NEURORADIOLOGY,
1982,
24
(01)
: 33
-
42
[4]
REVERSAL OF EARLY NEUROLOGIC AND NEURORADIOLOGICAL MANIFESTATIONS OF X-LINKED ADRENOLEUKODYSTROPHY BY BONE-MARROW TRANSPLANTATION
AUBOURG, P
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
AUBOURG, P
BLANCHE, S
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
BLANCHE, S
JAMBAQUE, I
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
JAMBAQUE, I
ROCCHICCIOLI, F
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
ROCCHICCIOLI, F
KALIFA, G
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
KALIFA, G
NAUDSAUDREAU, C
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
NAUDSAUDREAU, C
ROLLAND, MO
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
ROLLAND, MO
DEBRE, M
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
DEBRE, M
CHAUSSAIN, JL
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
CHAUSSAIN, JL
GRISCELLI, C
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
GRISCELLI, C
FISCHER, A
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
FISCHER, A
BOUGNERES, PF
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
BOUGNERES, PF
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1990,
322
(26)
: 1860
-
1866
[5]
AUBOURG P, 1987, ANN NEUROL, V21, P240
[6]
AUBOURG PR, 1988, AM J HUM GENET, V42, P408
[7]
BIGAZZI PE, 1990, AUTOIMMUNE DISEASES, P297
[8]
NERVONIC ACID BIOSYNTHESIS BY ERUCYL-COA ELONGATION IN NORMAL AND QUAKING MOUSE-BRAIN MICROSOMES - ELONGATION OF OTHER UNSATURATED FATTY ACYL-COAS (MONO AND POLY-UNSATURATED)
BOURRE, JM
论文数:
0
引用数:
0
h-index:
0
机构:
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
BOURRE, JM
DAUDU, O
论文数:
0
引用数:
0
h-index:
0
机构:
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
DAUDU, O
BAUMANN, N
论文数:
0
引用数:
0
h-index:
0
机构:
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
BAUMANN, N
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1976,
424
(01)
: 1
-
7
[9]
SPASTIC PARAPLEGIA ASSOCIATED WITH ADDISONS-DISEASE - ADULT VARIANT OF ADRENO-LEUKODYSTROPHY
BUDKA, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV VIENNA,INST NEUROL,A-1090 VIENNA,AUSTRIA
BUDKA, H
SLUGA, E
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV VIENNA,INST NEUROL,A-1090 VIENNA,AUSTRIA
SLUGA, E
HEISS, WD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV VIENNA,INST NEUROL,A-1090 VIENNA,AUSTRIA
HEISS, WD
[J].
JOURNAL OF NEUROLOGY,
1976,
213
(03)
: 237
-
250
[10]
PROGRESSION OF ENDOCRINOLOGICAL AND NEUROLOGICAL DYSFUNCTION IN ADRENOLEUKODYSTROPHY - ENDOCRINOLOGICAL EVIDENCE OF AN AFFECTION OF THE ADRENAL-CORTEX INDEPENDENT OF THE CEREBRAL DISORDER
DEWEERD, AW
论文数:
0
引用数:
0
h-index:
0
机构:
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
DEWEERD, AW
VANHUFFELEN, AC
论文数:
0
引用数:
0
h-index:
0
机构:
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
VANHUFFELEN, AC
REESER, HM
论文数:
0
引用数:
0
h-index:
0
机构:
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
REESER, HM
[J].
EUROPEAN NEUROLOGY,
1982,
21
(02)
: 117
-
123
←
1
2
3
4
5
6
7
8
→
共 73 条
[1]
AUBOURG P, 1990, AM J HUM GENET, V46, P459
[2]
MRI DETECTS CEREBRAL INVOLVEMENT IN NEUROLOGICALLY ASYMPTOMATIC PATIENTS WITH ADRENOLEUKODYSTROPHY
AUBOURG, P
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
AUBOURG, P
SELLIER, N
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
SELLIER, N
CHAUSSAIN, JL
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
CHAUSSAIN, JL
KALIFA, G
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
HOP ST VINCENT DE PAUL,INSERM,U188,F-75674 PARIS 14,FRANCE
KALIFA, G
[J].
NEUROLOGY,
1989,
39
(12)
: 1619
-
1621
[3]
ADRENOLEUKODYSTROPHY - ITS DIVERSE CT APPEARANCES AND AN EVOLUTIVE OR PHENOTYPIC VARIANT - THE LEUKODYSTROPHY WITHOUT ADRENAL INSUFFICIENCY
AUBOURG, P
论文数:
0
引用数:
0
h-index:
0
机构:
FOCH HOSP,DEPT NEURORADIOL,F-92150 SURESNES,FRANCE
AUBOURG, P
DIEBLER, C
论文数:
0
引用数:
0
h-index:
0
机构:
FOCH HOSP,DEPT NEURORADIOL,F-92150 SURESNES,FRANCE
DIEBLER, C
[J].
NEURORADIOLOGY,
1982,
24
(01)
: 33
-
42
[4]
REVERSAL OF EARLY NEUROLOGIC AND NEURORADIOLOGICAL MANIFESTATIONS OF X-LINKED ADRENOLEUKODYSTROPHY BY BONE-MARROW TRANSPLANTATION
AUBOURG, P
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
AUBOURG, P
BLANCHE, S
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
BLANCHE, S
JAMBAQUE, I
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
JAMBAQUE, I
ROCCHICCIOLI, F
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
ROCCHICCIOLI, F
KALIFA, G
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
KALIFA, G
NAUDSAUDREAU, C
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
NAUDSAUDREAU, C
ROLLAND, MO
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
ROLLAND, MO
DEBRE, M
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
DEBRE, M
CHAUSSAIN, JL
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
CHAUSSAIN, JL
GRISCELLI, C
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
GRISCELLI, C
FISCHER, A
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
FISCHER, A
BOUGNERES, PF
论文数:
0
引用数:
0
h-index:
0
机构:
HOP ST VINCENT DE PAUL,DEPT PEDIAT ENDOCRINOL,F-75674 PARIS 14,FRANCE
BOUGNERES, PF
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1990,
322
(26)
: 1860
-
1866
[5]
AUBOURG P, 1987, ANN NEUROL, V21, P240
[6]
AUBOURG PR, 1988, AM J HUM GENET, V42, P408
[7]
BIGAZZI PE, 1990, AUTOIMMUNE DISEASES, P297
[8]
NERVONIC ACID BIOSYNTHESIS BY ERUCYL-COA ELONGATION IN NORMAL AND QUAKING MOUSE-BRAIN MICROSOMES - ELONGATION OF OTHER UNSATURATED FATTY ACYL-COAS (MONO AND POLY-UNSATURATED)
BOURRE, JM
论文数:
0
引用数:
0
h-index:
0
机构:
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
BOURRE, JM
DAUDU, O
论文数:
0
引用数:
0
h-index:
0
机构:
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
DAUDU, O
BAUMANN, N
论文数:
0
引用数:
0
h-index:
0
机构:
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
HOP SALPETRIERE,INSERM,U 134,LAB NEUROCHIM,47 BLD HOP,75634 PARIS,FRANCE
BAUMANN, N
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1976,
424
(01)
: 1
-
7
[9]
SPASTIC PARAPLEGIA ASSOCIATED WITH ADDISONS-DISEASE - ADULT VARIANT OF ADRENO-LEUKODYSTROPHY
BUDKA, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV VIENNA,INST NEUROL,A-1090 VIENNA,AUSTRIA
BUDKA, H
SLUGA, E
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV VIENNA,INST NEUROL,A-1090 VIENNA,AUSTRIA
SLUGA, E
HEISS, WD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV VIENNA,INST NEUROL,A-1090 VIENNA,AUSTRIA
HEISS, WD
[J].
JOURNAL OF NEUROLOGY,
1976,
213
(03)
: 237
-
250
[10]
PROGRESSION OF ENDOCRINOLOGICAL AND NEUROLOGICAL DYSFUNCTION IN ADRENOLEUKODYSTROPHY - ENDOCRINOLOGICAL EVIDENCE OF AN AFFECTION OF THE ADRENAL-CORTEX INDEPENDENT OF THE CEREBRAL DISORDER
DEWEERD, AW
论文数:
0
引用数:
0
h-index:
0
机构:
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
DEWEERD, AW
VANHUFFELEN, AC
论文数:
0
引用数:
0
h-index:
0
机构:
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
VANHUFFELEN, AC
REESER, HM
论文数:
0
引用数:
0
h-index:
0
机构:
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
JULIANA KINDERZIEKENHUIS,THE HAGUE,NETHERLANDS
REESER, HM
[J].
EUROPEAN NEUROLOGY,
1982,
21
(02)
: 117
-
123
←
1
2
3
4
5
6
7
8
→