VIRUS-ASSOCIATED HEMOPHAGOCYTIC SYNDROME - FURTHER EVIDENCE FOR A T-CELL MEDIATED DISORDER

被引:30
作者
WATSON, HG [1 ]
GOULDEN, NJ [1 ]
MANSON, LM [1 ]
MCDERMID, G [1 ]
GRAY, TA [1 ]
PARKER, AC [1 ]
机构
[1] CITY HOSP EDINBURGH,REG INFECT DIS UNIT,EDINBURGH,MIDLOTHIAN,SCOTLAND
关键词
HEMOPHAGOCYTIC SYNDROME; VIRUS; T-CELL MEDIATED DISORDER;
D O I
10.1111/j.1365-2141.1994.tb03282.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A 16-year-old youth with life-threatening virus-associated haemophagocytic syndrome (VAHS) responded remarkably to treatment with cyclosporin A during two periods of active disease, the second of which was due to noncompliance with treatment. Our clinical observations support the hypothesis that VAHS is cytokine driven as a result of an aberrant T-cell response to infection.
引用
收藏
页码:213 / 215
页数:3
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