BIOSYNTHESIS AND MATURATION OF GLUCOCEREBROSIDASE IN GAUCHER FIBROBLASTS

被引:79
作者
JONSSON, LMV
MURRAY, GJ
SORRELL, SH
STRIJLAND, A
AERTS, JFGM
GINNS, EI
BARRANGER, JA
TAGER, JM
SCHRAM, AW
机构
[1] UNIV AMSTERDAM,INTERSUBFAC VAKGRP BIOCHEM,BIOCHEM LAB,POB 20151,1000 HD AMSTERDAM,NETHERLANDS
[2] NINCDS,MOLEC GENET LAB,MOLEC & MED GENET SECT,BETHESDA,MD 20205
来源
EUROPEAN JOURNAL OF BIOCHEMISTRY | 1987年 / 164卷 / 01期
关键词
D O I
10.1111/j.1432-1033.1987.tb11008.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:171 / 179
页数:9
相关论文
共 47 条
  • [1] AERTS JMF, 1986, ENZYMES LIPID METABO, P747
  • [2] THE OCCURRENCE OF 2 IMMUNOLOGICALLY DISTINGUISHABLE BETA-GLUCOCEREBROSIDASES IN HUMAN SPLEEN
    AERTS, JMFG
    DONKERKOOPMAN, WE
    VANDERVLIET, MK
    JONSSON, LMV
    GINNS, EI
    MURRAY, GJ
    BARRANGER, JA
    TAGER, JM
    SCHRAM, AW
    [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1985, 150 (03): : 565 - 574
  • [3] A PROCEDURE FOR THE RAPID PURIFICATION IN HIGH-YIELD OF HUMAN GLUCOCEREBROSIDASE USING IMMUNOAFFINITY CHROMATOGRAPHY WITH MONOCLONAL-ANTIBODIES
    AERTS, JMFG
    DONKERKOOPMAN, WE
    MURRAY, GJ
    BARRANGER, JA
    TAGER, JM
    SCHRAM, AW
    [J]. ANALYTICAL BIOCHEMISTRY, 1986, 154 (02) : 655 - 663
  • [4] MONOCLONAL-ANTIBODIES AGAINST HUMAN BETA-GLUCOCEREBROSIDASE
    BARNEVELD, RA
    TEGELAERS, FPW
    GINNS, EI
    VISSER, P
    LAANEN, EA
    BRADY, RO
    GALJAARD, H
    BARRANGER, JA
    REUSER, AJJ
    TAGER, JM
    [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1983, 134 (03): : 585 - 589
  • [5] BARRANGER JA, 1984, MOL BASIS LYSOSOMAL, P311
  • [6] BEUTLER E, 1970, J LAB CLIN MED, V76, P747
  • [8] BEUTLER E, 1976, AM J HUM GENET, V28, P62
  • [9] BEUTLER E, 1984, P NATL ACAD SCI US, V81, P6056
  • [10] Brady R. O., 1983, METABOLIC BASIS INHE, P842