REPLACEMENT THERAPY OF ALPHA-1-ANTITRYPSIN DEFICIENCY - REVERSAL OF PROTEASE-ANTIPROTEASE IMBALANCE WITHIN THE ALVEOLAR STRUCTURES OF PIZ SUBJECTS

被引：255

作者：

GADEK, JE ^{[1
]}

KLEIN, HG ^{[1
]}

HOLLAND, PV ^{[1
]}

CRYSTAL, RG ^{[1
]}

机构：

[1] NIH, CTR CLIN, BLOOD BANK, BETHESDA, MD 20205 USA

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1981年 / 68卷 / 05期

关键词：

D O I：

10.1172/JCI110360

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：1158 / 1165

页数：8

共 36 条

[1]

ALLEN RC, 1974, AM J CLIN PATHOL, V62, P732

[2]

CAWLEY LP, 1978, AM SOC CLIN PATHOL, P16

[3]

COHEN AB, 1979, AM REV RESPIR DIS, V120, P723

[4]

COX DW, 1976, AM REV RESPIR DIS, V113, P601

[5]

ERIKSSON S, 1964, ACTA MED SCAND, V175, P197

[6] CIGARETTE-SMOKING INDUCES FUNCTIONAL ANTIPROTEASE DEFICIENCY IN THE LOWER RESPIRATORY-TRACT OF HUMANS [J].

GADEK, JE ;

FELLS, GA ;

CRYSTAL, RG .

SCIENCE, 1979, 206 (4424) :1315-1316

[7] REPLACEMENT THERAPY IN HEREDITARY ANGIOEDEMA - SUCCESSFUL TREATMENT OF ACUTE EPISODES OF ANGIOEDEMA WITH PARTLY PURIFIED C1-INHIBITOR [J].

GADEK, JE ;

HOSEA, SW ;

GELFAND, JA ;

SANTAELLA, M ;

WICKERHAUSER, M ;

TRIANTAPHYLLOPOULOS, DC ;

FRANK, MM .

NEW ENGLAND JOURNAL OF MEDICINE, 1980, 302 (10) :542-546

[8] HUMAN NEUTROPHIL ELASTASE FUNCTIONS AS A TYPE-III COLLAGEN COLLAGENASE [J].

GADEK, JE ;

FELLS, GA ;

WRIGHT, DG ;

CRYSTAL, RG .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1980, 95 (04) :1815-1822

[9]

GADEK JE, J CLIN INVEST, V68

[10] PULMONARY-FUNCTION IN NON-SMOKING SUBJECTS WITH ALPHA1 ANTITRYPSIN DEFICIENCY (MZ PHENOTYPE) [J].

GELB, AF ;

KLEIN, E ;

LIEBERMAN, J .

AMERICAN JOURNAL OF MEDICINE, 1977, 62 (01) :93-98

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