LARGE ALTERATIONS IN GANGLIOSIDE AND NEUTRAL GLYCOSPHINGOLIPID PATTERNS IN BRAINS FROM CASES WITH INFANTILE NEURONAL CEROID LIPOFUSCINOSIS POLYUNSATURATED FATTY-ACID LIPIDOSIS

被引:52
作者
SVENNERHOLM, L
FREDMAN, P
JUNGBJER, B
MANSSON, JE
RYNMARK, BM
BOSTROM, K
HAGBERG, B
NOREN, L
SANTAVUORI, P
机构
[1] GOTHENBURG UNIV,DEPT FORENS MED,S-41124 GOTHENBURG,SWEDEN
[2] GOTHENBURG UNIV,E HOSP,S-41124 GOTHENBURG,SWEDEN
[3] CENT HOSP VASTERAS,CTR HABILITAT,VASTERAS,SWEDEN
[4] UNIV HELSINKI,CHILDRENS HOSP,SF-00100 HELSINKI 10,FINLAND
关键词
D O I
10.1111/j.1471-4159.1987.tb02435.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1772 / 1783
页数:12
相关论文
共 32 条
[2]   SEPARATION OF GANGLIOSIDES ON A NEW TYPE OF ANION-EXCHANGE RESIN [J].
FREDMAN, P ;
NILSSON, O ;
TAYOT, JL ;
SVENNERHOLM, L .
BIOCHIMICA ET BIOPHYSICA ACTA, 1980, 618 (01) :42-52
[3]   A NOVEL DISIALOGANGLIOSIDE (IV3NEUACIII6NEUACLC4) OF HUMAN ADENOCARCINOMA AND THE MONOCLONAL-ANTIBODY (FH9) DEFINING THIS DISIALOSYL STRUCTURE [J].
FUKUSHI, Y ;
NUDELMAN, E ;
LEVERY, SB ;
HIGUCHI, T ;
HAKOMORI, S .
BIOCHEMISTRY, 1986, 25 (10) :2859-2866
[4]   LATE INFANTILE PROGRESSIVE ENCEPHALOPATHY WITH DISTURBED POLYUNSATURATED FAT METABOLISM [J].
HAGBERG, B ;
SOURANDER, P ;
SVENNERHOLM, L .
ACTA PAEDIATRICA SCANDINAVICA, 1968, 57 (06) :495-+
[5]   POLYUNSATURATED FATTY-ACID LIPIDOSIS INFANTILE FORM OF SO-CALLED NEURONAL CEROIDLIPOFUSCINOSIS [J].
HAGBERG, B ;
HALTIA, M ;
SOURANDER, P ;
SVENNERHOLM, L ;
EEGOLOFS.O .
ACTA PAEDIATRICA SCANDINAVICA, 1974, 63 (05) :753-763
[6]   INFANTILE TYPE OF SO-CALLED NEURONAL CEROID-LIPOFUSCINOSIS - HISTOLOGICAL AND ELECTRON-MICROSCOPIC STUDIES [J].
HALTIA, M ;
RAPOLA, J ;
SANTAVUORI, P .
ACTA NEUROPATHOLOGICA, 1973, 26 (02) :157-170
[7]   IMMUNOCHEMISTRY OF THE LEWIS BLOOD-GROUP SYSTEM - ISOLATION AND STRUCTURES OF LEWIS-C ACTIVE AND RELATED GLYCOSPHINGOLIPIDS FROM THE PLASMA OF BLOOD-GROUP-O LE(A-B-) NONSECRETORS [J].
HANFLAND, P ;
KORDOWICZ, M ;
PETERKATALINIC, J ;
PFANNSCHMIDT, G ;
CRAWFORD, RJ ;
GRAHAM, HA ;
EGGE, H .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1986, 246 (02) :655-672
[8]   ULTRASTRUCTURAL LOCALIZATION OF CELL-MEMBRANE GM1 GANGLIOSIDE BY CHOLERA TOXIN - (IMMUNOELECTRON MICROSCOPY MEMBRANE RECEPTOR VIBRIO-CHOLERAE SIALIDASE GANGLIOSIDE TITRATION) [J].
HANSSON, HA ;
HOLMGREN, J ;
SVENNERHOLM, L .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1977, 74 (09) :3782-3786
[9]   GANGLIOSIDES OF HUMAN, BOVINE AND RABBIT RETINA [J].
HOLM, M ;
VANIER, MT ;
SVENNERH.L ;
MANSSON, JE .
BIOCHIMICA ET BIOPHYSICA ACTA, 1972, 280 (02) :356-&
[10]   HIGH-LEVELS OF BRAIN DOLICHOLS IN NEURONAL CEROID-LIPOFUSCINOSIS AND SENESCENCE [J].
KIN, NMKNY ;
PALO, J ;
HALTIA, M ;
WOLFE, LS .
JOURNAL OF NEUROCHEMISTRY, 1983, 40 (05) :1465-1473