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INTRACELLULAR AND EXTRACELLULAR ALPHA-D-MANNOSIDASE ACTIVITY OF CULTURED SKIN FIBROBLASTS - RELATIONSHIP TO CYSTIC-FIBROSIS
被引:13
作者
:
BUTTERWORTH, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH8 9YL,MIDLOTHIAN,SCOTLAND
UNIV EDINBURGH,EDINBURGH EH8 9YL,MIDLOTHIAN,SCOTLAND
BUTTERWORTH, J
[
1
]
机构
:
[1]
UNIV EDINBURGH,EDINBURGH EH8 9YL,MIDLOTHIAN,SCOTLAND
来源
:
CLINICA CHIMICA ACTA
|
1980年
/ 108卷
/ 03期
关键词
:
D O I
:
10.1016/0009-8981(80)90340-X
中图分类号
:
R446 [实验室诊断];
R-33 [实验医学、医学实验];
学科分类号
:
1001 ;
摘要
:
引用
收藏
页码:347 / 353
页数:7
相关论文
共 10 条
[1]
ALHADEFF JA, 1978, CLIN GENET, V14, P189
[2]
CARBOXYPEPTIDASE-B ACTIVITY OF CULTURED SKIN FIBROBLASTS AND RELATIONSHIP TO CYSTIC-FIBROSIS
BUTTERWORTH, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
BUTTERWORTH, J
DUNCAN, JJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
DUNCAN, JJ
[J].
CLINICA CHIMICA ACTA,
1979,
97
(01)
: 39
-
43
[3]
PRIMARY AMNIOTIC-FLUID CELL, SKIN FIBROBLAST AND LIVER ALPHA-L-FUCOSIDASE AND ITS RELATION TO CYSTIC-FIBROSIS
BUTTERWORTH, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH, EDINBURGH EH8 9YL, MIDLOTHIAN, SCOTLAND
UNIV EDINBURGH, EDINBURGH EH8 9YL, MIDLOTHIAN, SCOTLAND
BUTTERWORTH, J
GUY, GJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH, EDINBURGH EH8 9YL, MIDLOTHIAN, SCOTLAND
UNIV EDINBURGH, EDINBURGH EH8 9YL, MIDLOTHIAN, SCOTLAND
GUY, GJ
[J].
CLINICA CHIMICA ACTA,
1979,
92
(02)
: 109
-
116
[4]
GODSON GN, 1970, ANAL BIOCHEM, V35, P66
[5]
HARRIS A, 1979, LANCET, V2, P1371
[6]
HIRANI S, 1979, LANCET, V2, P906
[7]
HOSLI, 1979, LANCET, V2, P543
[8]
CYSTIC-FIBROSIS - DECREASED THERMOSTABILITY OF ALPHA-MANNOSIDASE IN CRUDE EXTRACELLULAR FLUIDS OF PATIENTS AND CARRIERS
HOSLI, P
论文数:
0
引用数:
0
h-index:
0
机构:
Institut Pasteur, Dépt de Biologie Moléculaire
HOSLI, P
VOGT, E
论文数:
0
引用数:
0
h-index:
0
机构:
Institut Pasteur, Dépt de Biologie Moléculaire
VOGT, E
[J].
FEBS LETTERS,
1979,
104
(02)
: 271
-
274
[9]
NORMAL EXTRACELLULAR EXCRETION OF ACIDIC ALPHA-MANNOSIDASE ACTIVITY BY MANNOSIDOSIS FIBROBLAST-CULTURES
HULTBERG, B
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV LUND HOSP,DEPT CLIN CHEM,S-22185 LUND,SWEDEN
UNIV LUND HOSP,DEPT CLIN CHEM,S-22185 LUND,SWEDEN
HULTBERG, B
MASSON, PK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV LUND HOSP,DEPT CLIN CHEM,S-22185 LUND,SWEDEN
UNIV LUND HOSP,DEPT CLIN CHEM,S-22185 LUND,SWEDEN
MASSON, PK
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1977,
481
(02)
: 573
-
577
[10]
PATRICK AD, 1979, LANCET, V2, P1015
←
1
→
共 10 条
[1]
ALHADEFF JA, 1978, CLIN GENET, V14, P189
[2]
CARBOXYPEPTIDASE-B ACTIVITY OF CULTURED SKIN FIBROBLASTS AND RELATIONSHIP TO CYSTIC-FIBROSIS
BUTTERWORTH, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
BUTTERWORTH, J
DUNCAN, JJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
UNIV EDINBURGH,EDINBURGH EH9 1LF,SCOTLAND
DUNCAN, JJ
[J].
CLINICA CHIMICA ACTA,
1979,
97
(01)
: 39
-
43
[3]
PRIMARY AMNIOTIC-FLUID CELL, SKIN FIBROBLAST AND LIVER ALPHA-L-FUCOSIDASE AND ITS RELATION TO CYSTIC-FIBROSIS
BUTTERWORTH, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH, EDINBURGH EH8 9YL, MIDLOTHIAN, SCOTLAND
UNIV EDINBURGH, EDINBURGH EH8 9YL, MIDLOTHIAN, SCOTLAND
BUTTERWORTH, J
GUY, GJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV EDINBURGH, EDINBURGH EH8 9YL, MIDLOTHIAN, SCOTLAND
UNIV EDINBURGH, EDINBURGH EH8 9YL, MIDLOTHIAN, SCOTLAND
GUY, GJ
[J].
CLINICA CHIMICA ACTA,
1979,
92
(02)
: 109
-
116
[4]
GODSON GN, 1970, ANAL BIOCHEM, V35, P66
[5]
HARRIS A, 1979, LANCET, V2, P1371
[6]
HIRANI S, 1979, LANCET, V2, P906
[7]
HOSLI, 1979, LANCET, V2, P543
[8]
CYSTIC-FIBROSIS - DECREASED THERMOSTABILITY OF ALPHA-MANNOSIDASE IN CRUDE EXTRACELLULAR FLUIDS OF PATIENTS AND CARRIERS
HOSLI, P
论文数:
0
引用数:
0
h-index:
0
机构:
Institut Pasteur, Dépt de Biologie Moléculaire
HOSLI, P
VOGT, E
论文数:
0
引用数:
0
h-index:
0
机构:
Institut Pasteur, Dépt de Biologie Moléculaire
VOGT, E
[J].
FEBS LETTERS,
1979,
104
(02)
: 271
-
274
[9]
NORMAL EXTRACELLULAR EXCRETION OF ACIDIC ALPHA-MANNOSIDASE ACTIVITY BY MANNOSIDOSIS FIBROBLAST-CULTURES
HULTBERG, B
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV LUND HOSP,DEPT CLIN CHEM,S-22185 LUND,SWEDEN
UNIV LUND HOSP,DEPT CLIN CHEM,S-22185 LUND,SWEDEN
HULTBERG, B
MASSON, PK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV LUND HOSP,DEPT CLIN CHEM,S-22185 LUND,SWEDEN
UNIV LUND HOSP,DEPT CLIN CHEM,S-22185 LUND,SWEDEN
MASSON, PK
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1977,
481
(02)
: 573
-
577
[10]
PATRICK AD, 1979, LANCET, V2, P1015
←
1
→